Atmaca Sezgin, Guler Arda, Türkmen İrem, Aydın Sinem, Ustundag Songul, Guler Gamze Babur
Istanbul Mehmet Akif Ersoy Thoracic and Cardiovascular Surgery Training and Research Hospital, Department of Cardiology, Istanbul, Turkey.
Istanbul Mehmet Akif Ersoy Thoracic and Cardiovascular Surgery Training and Research Hospital, Department of Radiology, Istanbul, Turkey.
J Cardiovasc Thorac Res. 2025 Mar 18;17(1):66-69. doi: 10.34172/jcvtr.025.33140. eCollection 2025 Mar.
Herein we present a case of a right ventricular (RV) thrombus in a patient with arrhythmogenic cardiomyopathy (ACM). The 24-year old female patient was diagnosed with ACM after echocardiography, genetic test and cardiac magnetic resonance imaging. Interestingly, at echocardiography, an unusal thrombus formation was detected at RV lateral wall. Also, CMR confirmed the thrombus and oral anticoagulant therapy was started. During the patient's follow-ups, it was observed that the imaging consistent with the reported thrombus disappeared after effective anticoagulant treatment. After the diagnosis was confirmed with genetic tests, an implantable cardioverter-defibrillator (ICD) was implanted in the patient with a high sudden cardiac death (SCD) risk score. Even in arrhythmogenic right ventricular cardiomyopathy patients thrombi are rarely reported. However, the development of imaging techniques may enable more frequent detection and effective treatment of thrombi in these patients.
在此,我们报告一例致心律失常性心肌病(ACM)患者出现右心室(RV)血栓的病例。该24岁女性患者经超声心动图、基因检测和心脏磁共振成像检查后被诊断为ACM。有趣的是,在超声心动图检查中,于右心室侧壁发现了异常血栓形成。此外,心脏磁共振成像证实了血栓的存在,并开始了口服抗凝治疗。在患者的随访过程中,观察到经有效抗凝治疗后,与报告的血栓相符的影像学表现消失。在基因检测确诊后,为该具有高心脏性猝死(SCD)风险评分的患者植入了植入式心脏复律除颤器(ICD)。即使在致心律失常性右心室心肌病患者中,血栓也很少被报道。然而,成像技术的发展可能使这些患者中血栓的检测更为频繁且治疗更有效。