Holemans C, Quaniers J, Boesmans E, Kerzmann A, Honoré P, Defraigne J O
Service de Chirurgie cardiovasculaire, CHU Liège, Belgique.
Service de Chirurgie abdominale, CHU Liège, Belgique.
Rev Med Liege. 2020 Jul;75(7-8):541-543.
Cystic lymphangioma is a rare and benign lymphatic malformation found most often in the first two years of life. Clinical manifestations are diverse and depend on size and site of the lesion. The most frequently affected sites are cervicofacial and axillary areas. The retroperitoneal form is rare. Diagnosis requires imaging but can only be confirmed on the basis of an anatomopathological examination. The treatment of choice is complete surgical removal. However, this is not always feasible due to proximity of vital structures. Some alternative therapies like sclerotic injection and oral drugs like immunosuppressive treatment or sildenafil are described. We report the case of a 62-year-old patient with retroperitoneal cystic lymphangioma successfully treated with sildenafil.
