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两例与急性和慢性髓系白血病相关的阴茎异常勃起的罕见表现:急诊处理

Unusual Presentation of Priapism Associated with Acute and Chronic Myeloid Leukemia in Two Patients: Emergency Management.

作者信息

Gaye Oumar, Thiam Ngor Mack, Cassell Ayun, Gueye Serigne Mourtalla, Sow Yaya, Fall Boubacar, Ndoye Alain Khassim

机构信息

Urology-Andrology Department, Hôpital Aristide Le Dantec, Senegal.

Urology-Andrology Department, Hôpital Général Idrissa Pouye, Senegal.

出版信息

Case Rep Urol. 2020 Aug 12;2020:4982432. doi: 10.1155/2020/4982432. eCollection 2020.

DOI:10.1155/2020/4982432
PMID:32855834
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC7442991/
Abstract

Priapism is a rare urological emergency. It is rarely a telltale sign of myeloid leukemia. We report two cases of acute myeloid leukemia in a child and chronic myeloid leukemia in a young adult presenting with priapism. Puncture irrigation of the corpora cavernosa followed by systemic treatment to lower the hyperviscosity of the blood due to leukemia provided optimal outcome. Prompt emergency management is required to lower the complication of erectile dysfunction.

摘要

阴茎异常勃起是一种罕见的泌尿外科急症。它很少是髓系白血病的特征性体征。我们报告了两例病例,一例是一名儿童患急性髓系白血病,另一例是一名年轻成人患慢性髓系白血病,均表现为阴茎异常勃起。对阴茎海绵体进行穿刺冲洗,随后进行全身治疗以降低白血病导致的血液高黏滞度,取得了最佳效果。需要迅速进行紧急处理以降低勃起功能障碍的并发症。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3034/7442991/eb600f89db26/CRIU2020-4982432.003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3034/7442991/6e235d30472d/CRIU2020-4982432.001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3034/7442991/a4c347d17b70/CRIU2020-4982432.002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3034/7442991/eb600f89db26/CRIU2020-4982432.003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3034/7442991/6e235d30472d/CRIU2020-4982432.001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3034/7442991/a4c347d17b70/CRIU2020-4982432.002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3034/7442991/eb600f89db26/CRIU2020-4982432.003.jpg

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Turk J Pediatr. 2019;61(2):311-312. doi: 10.24953/turkjped.2019.02.029.
2
Acute Lymphoblastic Leukemia in a Child Presenting Primarily with Priapism.一名主要以阴茎异常勃起为表现的儿童急性淋巴细胞白血病
J Indian Assoc Pediatr Surg. 2020 Jan-Feb;25(1):52-54. doi: 10.4103/jiaps.JIAPS_214_18. Epub 2019 Nov 27.
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Priapism secondary to chronic myeloid leukemia treated by a surgical cavernosa-corpus spongiosum shunt: Case report.
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EJHaem. 2022 Aug 27;3(4):1100-1115. doi: 10.1002/jha2.545. eCollection 2022 Nov.
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Clin Case Rep. 2021 Nov 19;9(11):e04901. doi: 10.1002/ccr3.4901. eCollection 2021 Nov.
经手术阴茎海绵体-尿道海绵体分流术治疗的慢性粒细胞白血病继发阴茎异常勃起:病例报告
Asian J Urol. 2019 Oct;6(4):373-376. doi: 10.1016/j.ajur.2018.12.004. Epub 2018 Dec 15.
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