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阴茎异常勃起作为慢性髓性白血病的首发表现:一例病例报告及文献综述

Priapism as the first manifestation in chronic myeloid leukemia: A case report and focused review of literature.

作者信息

Sossa Melo Claudia Lucia, Orozco Orozco Carlos Alberto, Peña Castellanos Angela Maria, Rueda Perea Maria Alejandra, Porras Bueno Cristian Orlando, Romero Diaz Carlos Ivan, Rojas Rodríguez Helga Natalia

机构信息

Servicio de Hemato-oncología Fundación Oftalmológica de Santander Facultad Ciencias de la Salud Universidad Autónoma de Bucaramanga Bucaramanga Colombia.

Servicio de Hemato-oncología Fundación Oftalmológica de Santander Programa para el Tratamiento y Estudio de Enfermedades Hematológicas y Oncológicas de Santander - PROTEHOS Bucaramanga Colombia.

出版信息

Clin Case Rep. 2021 Nov 19;9(11):e04901. doi: 10.1002/ccr3.4901. eCollection 2021 Nov.

DOI:10.1002/ccr3.4901
PMID:34824846
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC8603417/
Abstract

We report the case of a patient who was initially presented with ischemic priapism to the emergency department. He was treated with adrenaline intracavernous injections and aspiration with irrigation of the corpora cavernosa and distal shunt. In the postoperative period, anemia, basophilia, eosinophilia, thrombocytosis and hyperleukocytosis were detected. The patient was subsequently diagnosed with chronic myeloid leukemia. Priapism is a rare manifestation of chronic myeloid leukemia (≤ 3%) and occurs mostly due to hyperleukocytosis, resulting in thrombus formation and corporal venous outflow obstruction. Priapism occurring in any setting is considered as a medical emergency that requires immediate local therapy because of resulting irreversible cell damage and fibrosis if not treated within the first 24-48 h.

摘要

我们报告了一名最初因缺血性阴茎异常勃起被送至急诊科的患者病例。他接受了海绵体内注射肾上腺素以及海绵体冲洗抽吸和远端分流治疗。术后,检测到贫血、嗜碱性粒细胞增多、嗜酸性粒细胞增多、血小板增多和白细胞增多。该患者随后被诊断为慢性髓系白血病。阴茎异常勃起是慢性髓系白血病的一种罕见表现(≤3%),主要由于白细胞增多导致血栓形成和海绵体静脉流出道梗阻。在任何情况下发生的阴茎异常勃起都被视为医疗急症,由于如果在最初24 - 48小时内未得到治疗会导致不可逆的细胞损伤和纤维化,因此需要立即进行局部治疗。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/81f7/8603417/f7bb12d2030a/CCR3-9-e04901-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/81f7/8603417/f7bb12d2030a/CCR3-9-e04901-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/81f7/8603417/f7bb12d2030a/CCR3-9-e04901-g002.jpg

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本文引用的文献

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Acta Biomed. 2021 Jul 1;92(3):e2021193. doi: 10.23750/abm.v92i3.10796.
2
Unusual Presentation of Priapism Associated with Acute and Chronic Myeloid Leukemia in Two Patients: Emergency Management.两例与急性和慢性髓系白血病相关的阴茎异常勃起的罕见表现:急诊处理
Case Rep Urol. 2020 Aug 12;2020:4982432. doi: 10.1155/2020/4982432. eCollection 2020.
3
Priapism secondary to chronic myeloid leukemia treated by a surgical cavernosa-corpus spongiosum shunt: Case report.
经手术阴茎海绵体-尿道海绵体分流术治疗的慢性粒细胞白血病继发阴茎异常勃起:病例报告
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A rare presentation of chronic myeloid leukaemia with priapism treated with corporoglandular shunting.一例采用阴茎海绵体-尿道球腺分流术治疗的伴有阴茎异常勃起的慢性髓性白血病罕见病例。
Med J Malaysia. 2018 Dec;73(6):420-422.
5
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Urologic Management of Priapism Secondary to Chronic Myeloid Leukemia.慢性粒细胞白血病继发阴茎异常勃起的泌尿外科处理
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