Department of Medicine and.
Norris Comprehensive Cancer Center, Keck School of Medicine, University of Southern California, Los Angeles, California, USA.
J Clin Invest. 2020 Oct 1;130(10):5349-5369. doi: 10.1172/JCI133283.
Beclin 2 plays a critical role in metabolic regulation and obesity, but its functions in innate immune signaling and cancer development remain largely unknown. Here, we identified Beclin 2 as a critical negative regulator of inflammation and lymphoma development. Mice with homozygous ablation of BCL2-interacting protein 2 (Becn2) developed splenomegaly and lymphadenopathy and markedly increased ERK1/2 and NF-κB signaling for proinflammatory cytokine production. Beclin 2 targeted the key signaling kinases MEKK3 and TAK1 for degradation through an ATG9A-dependent, but ATG16L/Beclin 1/LC3-independent, autophagic pathway. Mechanistically, Beclin 2 recruited MEKK3 or TAK1 through ATG9A to form a complex (Beclin 2-ATG9A-MEKK3) on ATG9A+ vesicles upon ULK1 activation. Beclin 2 further interacted with STX5 and STX6 to promote the fusion of MEKK3- or TAK1-associated ATG9A+ vesicles to phagophores for subsequent degradation. Importantly, Becn2-deficient mice had a markedly increased incidence of lymphoma development, with persistent STAT3 activation. Myeloid-specific ablation of MEKK3 (Map3k3) completely rescued the phenotypes (splenomegaly, higher amounts of proinflammatory cytokines, and cancer incidence) of Becn2-deficient mice. Hence, our findings have identified an important role of Beclin 2 in the negative regulation of innate immune signaling and tumor development through an ATG9A-dependent, but ATG16L/Beclin 1/LC3-independent, autophagic pathway, thus providing a potential target for the treatment of inflammatory diseases and cancer.
Beclin 2 在代谢调节和肥胖中起着关键作用,但它在先天免疫信号和癌症发展中的功能在很大程度上仍然未知。在这里,我们确定 Beclin 2 是炎症和淋巴瘤发展的关键负调控因子。Beclin 2 基因纯合缺失的小鼠表现出脾肿大和淋巴结病,并显著增加 ERK1/2 和 NF-κB 信号,促进促炎细胞因子的产生。Beclin 2 通过一种依赖 ATG9A 但不依赖 ATG16L/Beclin 1/LC3 的自噬途径,靶向关键信号激酶 MEKK3 和 TAK1 进行降解。从机制上讲,Beclin 2 通过 ATG9A 招募 MEKK3 或 TAK1,在 ULK1 激活时,在 ATG9A+ 小泡上形成 Beclin 2-ATG9A-MEKK3 复合物。Beclin 2 还与 STX5 和 STX6 相互作用,促进与 MEKK3 或 TAK1 相关的 ATG9A+ 小泡与吞噬体融合,随后进行降解。重要的是,Becn2 基因缺失的小鼠淋巴瘤发展的发生率显著增加,STAT3 持续激活。髓系特异性 MEKK3(Map3k3)缺失完全挽救了 Becn2 基因缺失小鼠的表型(脾肿大、促炎细胞因子含量增加和癌症发生率增加)。因此,我们的研究结果表明,Beclin 2 通过一种依赖 ATG9A 但不依赖 ATG16L/Beclin 1/LC3 的自噬途径,在先天免疫信号和肿瘤发展的负调控中起着重要作用,为炎症性疾病和癌症的治疗提供了一个潜在的靶点。