Fan Ye-Hui, Tang He-Nan, Zhou Jian-Peng, Fang Qiang, Li Shu-Xuan, Kou Kai, Lv Guo-Yue
The First Hospital of Jilin University, Changchun, Jilin, China.
Medicine (Baltimore). 2020 Sep 4;99(36):e22077. doi: 10.1097/MD.0000000000022077.
Hepatic epithelioid hemangioendothelioma (HEH) is a rare vascular tumor of the liver with malignant potential. It can be of solitary type, multifocal type, or diffuse type. Although there are some characteristic features on radiologic imaging, the definitive diagnosis of HEH is based on histopathology. The surgical treatment of HEH includes liver resection and transplant.
A middle-aged woman presented with easy fatiguability and anorexia for 1 month was found to have multifocal lesions on radiological imaging.
HEH was diagnosed by needle biopsy. It can be seen from imaging that this case is a multifocal form. The largest lesion increased from 3 to 3.3 cm within 2 months, with an increase of 9.45%; no other relevant literatures have been reported.
The possibility of liver transplantation was suggested to the patient. However, the patient refused transplantation and was successfully treated by radical right hepatectomy and resection of the left lobe lesion.
She remained disease-free throughout a year follow-up period.
HEH is a rare disease with characteristic radiological and pathological features. Although liver transplantation is the preferred treatment for multifocal HEH, surgical excision represents one alternative when the lesions can be guaranteed to be completely excised.
肝上皮样血管内皮瘤（HEH）是一种具有恶性潜能的肝脏罕见血管肿瘤。它可分为孤立型、多灶型或弥漫型。尽管在放射影像学上有一些特征性表现，但HEH的确诊仍基于组织病理学。HEH的外科治疗包括肝切除和肝移植。
一名中年女性因1个月来易疲劳和食欲减退就诊，影像学检查发现有多灶性病变。
经穿刺活检诊断为HEH。从影像学上看，该病例为多灶型。最大病灶在2个月内从3 cm增大至3.3 cm，增大了9.45%；未见其他相关文献报道。
向患者建议了肝移植的可能性。然而，患者拒绝移植，随后行根治性右肝切除及左叶病灶切除，治疗成功。
在为期一年的随访期内，她未出现疾病复发。
HEH是一种具有特征性放射学和病理学表现的罕见疾病。尽管肝移植是多灶性HEH的首选治疗方法，但当病灶能够保证完全切除时，手术切除也是一种选择。
