Alomary Nawaf Abdulkareem, Albeeshi Majid Zaab, Al Thebaity Rasha Eidah, Yousef Zeyad Mohammed, El-Boghdadly Sami Abdelkereim
College of Medicine, King Saud Bin Abdulaziz University for Health Sciences, Riyadh, Saudi Arabia.
King Abdullah International Medical Research Center, Riyadh, Saudi Arabia.
J Surg Case Rep. 2020 Sep 5;2020(9):rjaa330. doi: 10.1093/jscr/rjaa330. eCollection 2020 Sep.
Aggressive angiomyxoma (AA) is an uncommon mesenchymal tumor that mainly affects the perineum and pelvis in females of reproductive age. AA is commonly misdiagnosed as a Bartholin's duct cyst, abscess or levator hernia. A 42-year-old female presented with a large, progressive and painless perineal swelling. She was initially diagnosed with an obturator hernia three times over the past 10 years and underwent multiple surgeries for recurrences. For this presentation, she underwent exploratory laparotomy. No hernia was identified. A large mass over the perineal area extending from the vulvar commissure to the anus was visualized. The diagnosis of AA was made on histopathology. Leuprolide (GnRHa) was used as hormonal therapy postoperatively. AA should be considered in any pelvic mass in a young female that recurs after excision. Prompt diagnosis will contribute toward minimizing local destruction of surrounding structures.
侵袭性血管黏液瘤（AA）是一种罕见的间叶性肿瘤，主要影响育龄女性的会阴和盆腔。AA常被误诊为巴氏腺管囊肿、脓肿或提肌疝。一名42岁女性出现一个逐渐增大、无痛的会阴肿物。在过去10年中，她最初三次被诊断为闭孔疝，并因复发接受了多次手术。此次就诊时，她接受了剖腹探查术。未发现疝。可见会阴区有一个从外阴联合延伸至肛门的巨大肿物。经组织病理学检查确诊为AA。术后使用亮丙瑞林（GnRHa）进行激素治疗。对于年轻女性切除后复发的任何盆腔肿物，都应考虑AA。及时诊断有助于尽量减少对周围结构的局部破坏。
