Munshi Faizanahmed I, Polotti Charles F, Elsamra Sammy E
Division of Urology, Rutgers Robert Wood Johnson Medical School, New Brunswick, New Jersey, USA.
J Endourol Case Rep. 2020 Sep 17;6(3):135-138. doi: 10.1089/cren.2019.0137. eCollection 2020.
Situs invesus totalis is a rare congenital anomaly characterized by the mirror-image transposition of abdominal and thoracic organs. Although feasible, operating on patients with situs inversus offers unique technical challenges to the surgeon because of its rarity and the contralateral disposition of the viscera. Urologists in particular need to be aware of the genitourinary abnormalities associated with situs inversus when planning to operate. We report the case of a 67-year-old man with invasive bladder cancer in the presence of situs inversus totalis (SIT) and associated bilateral duplicated ureters. This is only the second case of bladder cancer in the context of situs inversus reported in the literature and the first one managed with robot-assisted radical cystectomy and urinary diversion with an intracorporeal ileal conduit. In this unique case, robot-assisted radical cystectomy with intracorporeal ileal conduit in a patient with muscle-invasive bladder cancer and SIT was safely performed and we suggest to others to consider our technique of "mirror-image port placement and surgical technique" if they encounter such a patient.
完全性内脏反位是一种罕见的先天性异常,其特征为腹部和胸部器官呈镜像转位。尽管对完全性内脏反位患者进行手术是可行的,但由于其罕见性以及内脏的对侧分布,这给外科医生带来了独特的技术挑战。尤其是泌尿外科医生在计划手术时需要了解与完全性内脏反位相关的泌尿生殖系统异常情况。我们报告了一例67岁男性患者,患有浸润性膀胱癌,同时伴有完全性内脏反位(SIT)及双侧重复输尿管。这是文献中报道的第二例内脏反位合并膀胱癌的病例,也是首例采用机器人辅助根治性膀胱切除术及体内回肠代膀胱术进行治疗的病例。在这个独特的病例中,我们成功地为一名患有肌肉浸润性膀胱癌和完全性内脏反位的患者实施了机器人辅助根治性膀胱切除术及体内回肠代膀胱术,并且建议其他医生在遇到此类患者时考虑我们的“镜像端口放置和手术技术”。