Department of Neurosurgery, National Hospital Organization Kanazawa Medical Center, Kanazawa, 920-8650, Ishikawa, Japan.
Department of Neurosurgery, Kanazawa University Hospital, 13-1 Takara-machi, Kanazawa, 920-8641, Ishikawa, Japan.
Childs Nerv Syst. 2021 Aug;37(8):2667-2671. doi: 10.1007/s00381-020-04940-9. Epub 2020 Oct 27.
Spinal cord subependymomas (SCSEs) in children are extremely rare, and no reports distinguishing SCSEs from syringomyelia have been published. We report a case of a 10-year-old boy who presented with torticollis, scoliosis, as well as pain that had begun in the posterior portion of the neck and progressed to the right shoulder and upper arm. Magnetic resonance imaging showed an intramedullary cyst-like lesion with the same signal intensity as that of cerebrospinal fluid. Idiopathic syringomyelia with scoliosis was first suspected, and a syrinx-subarachnoid space shunt was performed. After surgery, the lesion was slightly smaller; however, 2 years after surgery, it had re-grown, causing excruciating pain but no other symptoms. A second surgery was performed, and gross total resection was achieved. Pathological evaluation revealed SCSE. SCSE needs to be considered as a differential diagnosis for spinal centric cyst-like lesions in children.
儿童脊髓室管膜下瘤（SCSEs）极为罕见，尚无将 SCSE 与脊髓空洞症区分开来的报道。我们报告了一例 10 岁男孩，他表现为斜颈、脊柱侧凸，以及始于颈部后部并进展至右肩部和上臂的疼痛。磁共振成像显示髓内囊肿样病变，与脑脊液信号强度相同。首先怀疑为特发性脊髓空洞症伴脊柱侧凸，并进行了脊髓空洞蛛网膜下腔分流术。手术后，病变略小；然而，手术后 2 年，病变再次生长，引起剧痛，但无其他症状。进行了第二次手术，实现了大体全切除。病理评估显示为 SCSE。SCSE 需要被视为儿童脊髓中心性囊样病变的鉴别诊断。
