Department of Cardiac Surgery, Careggi University Hospital, Florence, Italy.
Department of Diagnostic Cardiology, Careggi University Hospital, Florence, Italy.
Ann Thorac Surg. 2021 May;111(5):e319-e321. doi: 10.1016/j.athoracsur.2020.07.093. Epub 2020 Oct 29.
Chordoma is a rare tumor, usually diagnosed when the disease is advanced. Despite its slow growth, it is locally aggressive and has a poor long-term prognosis. Surgery is the mainstay treatment. Although cardiac metastases are very rare, the heart is frequently involved in systemic neoplastic diseases. This report describes a typical case of metastatic chordoma: the age at first diagnosis, the site of the primary tumor, and the slow growth of the cardiac metastasis were all typical features. Surgical excision of the mass from the right ventricular outflow tract is described together with echocardiographic, radiologic, and histopathologic characteristics of the metastatic chordoma.
软骨肉瘤是一种罕见的肿瘤，通常在疾病晚期才被诊断出来。尽管它生长缓慢，但具有局部侵袭性和较差的长期预后。手术是主要的治疗方法。尽管心脏转移非常罕见，但心脏经常涉及全身性肿瘤疾病。本报告描述了一个典型的转移性软骨肉瘤病例：首次诊断的年龄、原发性肿瘤的部位和心脏转移的缓慢生长均为典型特征。本文描述了从右心室流出道切除肿块的手术过程，并结合转移性软骨肉瘤的超声心动图、影像学和组织病理学特征进行了讨论。
