Elghareeb Manal Ms, Allah Mona Yy Abd, Abdallah Sieza S, Eldesoky Ahmed R, Halim Amal Af
Department of Clinical Oncology and Nuclear Medicine, Faculty of Medicine, Mansoura University, Mansoura, Egypt.
Department of Pathology, Faculty of Medicine, Mansoura University, Mansoura, Egypt.
J Orthop Case Rep. 2021 May;11(5):1-3. doi: 10.13107/jocr.2021.v11.i05.2180.
Chordoma is a malignant neoplasm that arises from notochord remnants. Its incidence is highest above the age of 50 and behaves as a locally aggressive tumor with a slow growth rate. In most cases, complete surgical resection followed by radiotherapy offers the best chance of control. Developing metachronous tumors or distant metastasis is uncommon.
A 56-year-old male patient of sacral chordoma was treated by surgery and radiotherapy. He developed later bilateral inguinal lymph node metastasis and metachronous clivus chordoma.
Chordomas are rare. Multiplicity of primary disease and distant metastasis could happen, so regular follow-up is warranted and more effective therapeutic modalities are needed.
脊索瘤是一种起源于脊索残余组织的恶性肿瘤。其发病率在50岁以上人群中最高，表现为局部侵袭性肿瘤，生长速度缓慢。在大多数情况下，完整的手术切除后辅以放疗提供了最佳的控制机会。发生异时性肿瘤或远处转移并不常见。
一名56岁的骶骨脊索瘤男性患者接受了手术和放疗。他后来出现双侧腹股沟淋巴结转移和异时性斜坡脊索瘤。
脊索瘤罕见。原发性疾病可能出现多发及远处转移，因此有必要进行定期随访，且需要更有效的治疗方式。
