Jang Nam, Shin Hyun Woo, Kim Junekyu, Yoon Kun Chul
Department of Plastic and Reconstructive Surgery, Kangbuk Samsung Hospital, Sungkyunkwan University School of Medicine, Seoul, Korea.
Arch Craniofac Surg. 2020 Oct;21(5):305-308. doi: 10.7181/acfs.2020.00304. Epub 2020 Oct 20.
Madelung's disease (MD) otherwise known as Launois-Bensaude syndrome, multiple symmetrical lipomatosis, or benign symmetric lipomatosis, is a rare disease characterized by abnormal diffuse lipomatosis in proximal upper limbs and neck. Here, we report a rare case of MD. A 66-year-old man presented with massive growth of soft tissues in the cervico-occipital region of more than 2 years duration. Physical examination showed diffuse enlargement of the anterior neck (Madelung's collar) and three huge humps at the posterior neck. Under a diagnosis of MD, lipectomy via a single anterior transverse incision and liposuction were performed. This rare case report may be helpful for assessing patients with abnormal diffuse lipomatosis in the neck and proximal upper limbs.
马德隆氏病(MD)又称劳诺瓦-本索德综合征、多发性对称性脂肪瘤病或良性对称性脂肪瘤病,是一种罕见疾病,其特征为上肢近端和颈部出现异常弥漫性脂肪瘤病。在此,我们报告一例罕见的马德隆氏病病例。一名66岁男性,颈枕部软组织大量生长超过2年。体格检查显示前颈部弥漫性肿大(马德隆氏项圈),后颈部有三个巨大隆起。在诊断为马德隆氏病后,通过单一前横切口进行了脂肪切除术和抽脂术。这一罕见病例报告可能有助于评估颈部和上肢近端出现异常弥漫性脂肪瘤病的患者。