Sohn Aaron J, Lang Benjamin, McCarroll Michael, Agarwal Atin
Department of Pathology, Baylor University Medical Center, Dallas, Texas.
Department of Radiology, Baylor University Medical Center, Dallas, Texas.
Proc (Bayl Univ Med Cent). 2020 Aug 19;33(4):646-648. doi: 10.1080/08998280.2020.1798723.
Ewing sarcoma/peripheral primitive neuroectodermal tumor (ES/pPNET) is a malignant small round cell sarcoma commonly occurring among children, adolescents, and adults. We report a rare case of ES/pPNET arising from the lung in a 49-year-old woman. She was found to have a mass in the right lung on a screening imaging study for her mutation. A lobectomy was performed and the mass had histological, immunohistochemical, and molecular features of ES/pPNET. Few cases of primary pulmonary Ewing sarcoma have been reported.
尤因肉瘤/外周原始神经外胚层肿瘤(ES/pPNET)是一种常见于儿童、青少年和成人的恶性小圆细胞肉瘤。我们报告了一例罕见的49岁女性肺部发生的ES/pPNET病例。她在针对其基因突变的筛查影像学检查中被发现右肺有一个肿块。进行了肺叶切除术,该肿块具有ES/pPNET的组织学、免疫组织化学和分子特征。原发性肺尤因肉瘤的病例报道较少。