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18F-FDG PET/CT 在波兰综合征和胃癌的罕见病例中的应用。

18F-FDG PET/CT in a Rare Case of Poland Syndrome and Gastric Cancer.

机构信息

From the Radiation Medicine Centre, Bhabha Atomic Research Centre, Mumbai, India.

出版信息

Clin Nucl Med. 2021 Apr 1;46(4):e195-e197. doi: 10.1097/RLU.0000000000003392.

DOI:10.1097/RLU.0000000000003392
PMID:33181754
Abstract

Poland syndrome is a rare congenital anomaly characterized by unilateral aplasia of the sternoclavicular head of pectoralis major muscle with varying degree of same side upper limb anomalies. A 44-year-old man, with a case of adenocarcinoma of stomach, whose CECT chest revealed complete absence of pectoralis major and minor muscles on the left side, was diagnosed with Poland syndrome without presence of typical ipsilateral limb anomalies. Follow-up PET/CT revealed metabolically active recurrent disease with typical findings of Poland syndrome. It is important to be aware of oncologic association in a patient of Poland syndrome as highlighted in the present case.

摘要

波兰氏综合征是一种罕见的先天性异常,其特征为单侧胸大肌胸锁关节头部分缺失,并伴有不同程度的同侧上肢异常。一名 44 岁男性,患有胃癌,胸部 CECT 显示左侧胸大肌和胸小肌完全缺失,诊断为波兰氏综合征,无典型同侧肢体异常。随访 PET/CT 显示复发性疾病有代谢活性,且具有典型的波兰氏综合征表现。在本病例中强调了波兰氏综合征患者的肿瘤相关性,因此了解这一点非常重要。

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Clin Nucl Med. 2021 Apr 1;46(4):e195-e197. doi: 10.1097/RLU.0000000000003392.
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