Celik Burçin
Department of Chest Surgery, Faculty of Medicine, Ondokuz Mayıs University, Samsun, Turkey.
Tuberk Toraks. 2010;58(2):173-6.
Poland's syndrome is an uncommon congenital anomaly characterized by unilateral absence of pectoralis major muscle, ipsilateral hand abnormalities, and a variety of associated anomalies. The incidence of the syndrome ranges from 1/7000 to 1/100.000. The syndrome is observed more frequently in man than in woman. A 22-years-old man who was admitted with a history of chest pain and dyspnea to our emergency department. On examination, breath sounds were decreased on the right side, there was an absence of the pectoralis major muscle, a shortness on the right upper limb and a restriction on the right shoulder and right elbow. Initially chest radiograph showed total pneumothorax on the right side. The patient was treated with tube thoracostomy. This case is presented to draw attention to the association of Poland syndrome with spontaneous pneumothorax.
波兰综合征是一种罕见的先天性异常,其特征为单侧胸大肌缺如、同侧手部畸形以及多种相关异常。该综合征的发病率在1/7000至1/100000之间。男性比女性更常观察到该综合征。一名22岁男性因胸痛和呼吸困难病史入住我院急诊科。检查发现右侧呼吸音减弱,胸大肌缺如,右上臂短小,右肩和右肘活动受限。最初胸部X线片显示右侧全气胸。患者接受了胸腔闭式引流术治疗。本文报告此病例以引起对波兰综合征与自发性气胸关联的关注。