Kuo I-Chun, Rutter Michael
Division of Pediatric Otolaryngology, Aerodigestive and Esophageal Center, Cincinnati Children's Hospital Medical Center, Cincinnati, OH, United States.
Department of Otolaryngology-Head and Neck Surgery, Chang Gung Memorial Hospital, Taoyuan, Taiwan.
Front Pediatr. 2020 Oct 19;8:555040. doi: 10.3389/fped.2020.555040. eCollection 2020.
Congenital webs are rare and represent <5% of all congenital laryngeal anomalies. They are usually a partial laryngeal atresia rather than a true web, and present as a thick and fibrotic web with subglottic extension and associated subglottic stenosis. All patients with a congenital anterior glottic web should be evaluated for chromosome 22q11.2 deletion syndrome. Management strategies are mainly based on the severity of airway obstruction and the anatomical extension of the webs. Simple division of the web endoscopically may be adequate for rare thin webs, however, an open approach is usually warranted for thick glottic webs regardless of Cohen grades. Open repair can be either with keel placement or reconstruction of the anterior commissure.
先天性喉蹼罕见,占所有先天性喉部异常的比例不到5%。它们通常是部分喉闭锁而非真正的喉蹼,表现为增厚且纤维化的喉蹼,伴有声门下延伸及相关的声门下狭窄。所有先天性前声门喉蹼患者均应评估是否患有22q11.2染色体缺失综合征。治疗策略主要基于气道梗阻的严重程度和喉蹼的解剖学延伸范围。对于罕见的薄喉蹼,单纯内镜下分离可能就足够了,然而,无论科恩分级如何,对于厚声门喉蹼通常都需要采用开放手术。开放修复可采用放置龙骨或重建前联合的方法。