Department of Pediatric & Congenital Heart Surgery, Fortis Escorts Heart Institute, New Delhi, India.
Department of Pediatric & Congenital Heart Sciences, Fortis Escorts Heart Institute, New Delhi, India.
Eur J Cardiothorac Surg. 2021 Apr 13;59(3):688-696. doi: 10.1093/ejcts/ezaa378.
To describe the morphology, echocardiographic features and surgical management of the entity appropriately described as 'double outlet of both ventricles'.
Seven patients (5 males, age 0.5-7.5 months) were diagnosed to have a unique form of subarterial ventricular septal defect (VSD) and ventriculo-arterial connection, where a muscular outlet septum straddled the crest of the ventricular septum in a cruciate manner, such that both great arteries were equally committed to both ventricles. Diagnosis was established by echocardiography, with 6 patients submitted to surgical repair by means of intracardiac routing of the left ventricle to the aorta using 2 patches.
Surgical repair was successful in all 6 patients in whom it was attempted. In addition, 1 patient underwent concomitant repair of aortic coarctation, and 2 had closure of multiple VSDs. We lost 1 patient to follow-up after diagnosis. Follow-up with a range from 3 months to 8 years in the remaining patients revealed all to be clinically well with satisfactory growth of both outflow tracts.
We describe a series of patients with the ventriculo-arterial connection best described as 'double outlet of both ventricles'. Diagnosis is readily established by echocardiography. Good early and midterm results can be expected subsequent to surgical repair using 2 patches for interventricular septation.
恰当地描述被描述为“双心室出口”的实体的形态、超声心动图特征和手术处理方法。
7 名患者（5 名男性，年龄 0.5-7.5 个月）被诊断为具有独特的亚室间隔缺损（VSD）和心室动脉连接形式，其中一个肌性流出间隔以十字形跨越室间隔嵴，使得两个大动脉都同样通向两个心室。诊断通过超声心动图确定，6 名患者通过使用 2 个补丁进行心内左心室到主动脉的路由手术修复。
在尝试手术修复的 6 名患者中，手术修复均成功。此外，1 名患者同时进行了主动脉缩窄修复，2 名患者进行了多个 VSD 的闭合。我们在诊断后失去了 1 名患者的随访。在其余患者中，随访时间从 3 个月到 8 年不等，所有患者均临床状况良好，流出道均有满意的生长。
我们描述了一系列具有最佳描述为“双心室出口”的心室动脉连接的患者。超声心动图可快速诊断。使用 2 个补丁进行室间隔分隔的手术修复后，可获得良好的早期和中期结果。
