Buge A, Vincent D, Rancurel G, Dechy H, Dorra M, Betourne C
Clinique Neurologique, Hôpital de la Salpêtrière, Paris.
Rev Neurol (Paris). 1987;143(12):832-5.
A case of multiple intracranial arterial aneurysms occurring in a 43 year-old patient with an 8-year history of Behcet's disease is reported. The diagnosis was based upon the past occurrence of polyarthritis, oral and scrotal aphthous ulcers and cutaneous hypersensitivity. There was a three year remission after a brief treatment with corticosteroids. At the end of this period, a left hemiplegia occurred. CT scan showed an infarction in the right middle cerebral artery territory. Angiography showed fusiform aneurysms of the intracranial right internal carotid, right anterior and middle cerebral arteries. The draining veins and sinuses were normal. Careful angiographic examination of visceral and peripheral arteries showed only bilateral retinal artery aneurysms. Large artery involvement is a rare complication of Behcet's disease, and a thorough review of the literature showed only one reported case of an intracranial aneurysm.
报告了一例43岁患有白塞病8年的患者发生多发性颅内动脉瘤的病例。诊断基于过去出现的多关节炎、口腔和阴囊阿弗他溃疡以及皮肤超敏反应。经皮质类固醇短暂治疗后有三年缓解期。在此期间结束时，出现了左侧偏瘫。CT扫描显示右侧大脑中动脉区域梗死。血管造影显示颅内右侧颈内动脉、右侧大脑前动脉和大脑中动脉呈梭形动脉瘤。引流静脉和静脉窦正常。对内脏和外周动脉进行仔细的血管造影检查仅发现双侧视网膜动脉动脉瘤。大动脉受累是白塞病的一种罕见并发症，对文献的全面回顾仅发现一例颅内动脉瘤的报告病例。
