da Costa Danilo-Viegas, de Araújo Vania-Eloisa, de Abreu Fernando-Antônio-Mauad, Souto Giovanna-Ribeiro
DDS, MDSc student. Department of Dentistry. Pontifical Catholic University of Minas Gerais.
DDS, MDSc, PhD. Department of Dentistry. Pontifical Catholic University of Minas Gerais.
J Clin Exp Dent. 2020 Dec 1;12(12):e1196-e1200. doi: 10.4317/jced.56642. eCollection 2020 Dec.
Thrombocytopenia-absent radius (TAR) syndrome is a congenital malformation in which affected individuals present reductions in the number of platelets, hypoplasia, or absence of radial bone unilaterally or bilaterally. Hematologic, skeletal, cardiac (particularly tetralogy of Fallot and septal-atrial defects), and gastrointestinal anomalies are most commonly associated with TAR syndrome. Skeletal changes result in a higher risk of dental and craniofacial trauma in patients with the syndrome. Thus, it is important for the dentist to be aware of the characteristics of TAR syndrome and its clinical management for better care of these patients. The objective of this study is to describe a case report of a 26-year-old patient with TAR syndrome with a history of trauma and root fracture of tooth 11 and alveolar bone ridge. During anamnesis, root fractures requiring the extraction of the 11 tooth, alveolar bone ridge fracture in the adjacent region, and dental trauma were observed. A hematological evaluation and blood and radiological examinations were performed. Osseointegrated implant was performed using the guided surgery and flapless technique, as well as prosthetic rehabilitation in the affected region. This report discusses the importance of careful planning, such as the use of incisions and conservative surgery, techniques for alveolar ridge preservation, gingival manipulation, and prosthesis confection. The patient was attended by a hematologist throughout the treatment. TAR syndrome, absent radii and thrombocytopenia, dental implants, oral surgery.
血小板减少伴桡骨缺如(TAR)综合征是一种先天性畸形,患病个体表现为血小板数量减少、发育不全,或单侧或双侧桡骨缺如。血液学、骨骼、心脏(尤其是法洛四联症和房间隔缺损)以及胃肠道异常最常与TAR综合征相关。骨骼变化导致该综合征患者发生牙齿和颅面部创伤的风险更高。因此,对于牙医而言,了解TAR综合征的特征及其临床管理方法对于更好地护理这些患者很重要。本研究的目的是描述一例26岁TAR综合征患者的病例报告,该患者有11号牙外伤和牙根骨折以及牙槽嵴的病史。在问诊期间,观察到需要拔除11号牙的牙根骨折、相邻区域的牙槽嵴骨折以及牙齿外伤。进行了血液学评估以及血液和影像学检查。采用引导式手术和无瓣技术植入骨整合种植体,并对患区进行了修复康复治疗。本报告讨论了精心规划的重要性,例如切口的使用和保守手术、牙槽嵴保存技术、牙龈处理以及义齿制作。在整个治疗过程中,有血液科医生对患者进行诊治。TAR综合征、桡骨缺如和血小板减少、牙种植体、口腔外科手术