Universidade Estadual Paulista Júlio de Mesquita Filho - Faculdade de Medicina de Botucatu - UNESP, Botucatu, SP - Brasil.
Arq Bras Cardiol. 2020 Nov;115(5):927-935. doi: 10.36660/abc.20190802.
Hypertrophic cardiomyopathy (HCM) is the most common heart disease with a genetic origin, and its main characteristic is left ventricular hypertrophy that occurs in the absence of other conditions that trigger this change. HCM may present from asymptomatic forms to manifestations of sudden cardiac death and severe heart failure. Contemporary high-resolution imaging methods and more accurate clinical scores have been used and developed to provide a prognostic assessment and adequate functional assessments, as well as to allow for the stratification of clinical severity. These aspects will be addressed in this review, along with other classic topics inherent to the study of this disease.
肥厚型心肌病(HCM)是最常见的具有遗传起源的心脏病,其主要特征是在不存在引发这种变化的其他条件的情况下出现左心室肥厚。HCM 可表现为无症状形式,也可表现为心源性猝死和严重心力衰竭。当代高分辨率成像方法和更准确的临床评分已被用于和开发,以提供预后评估和充分的功能评估,并允许对临床严重程度进行分层。本文将讨论这些方面,以及与该疾病研究相关的其他经典主题。