Nelson Jana, Wachowiak Robin, Siekmeyer Manuela, Knuepfer Matthias, Thome Ulrich, Holger Stepan, Lacher Martin
Division of Pediatric Surgery, Leipzig University Hospital for Children and Adolescents, Leipzig, Saxony, Germany.
Department of Pediatric Medicine, Leipzig University Hospital for Children and Adolescents, Leipzig, Saxony, Germany.
European J Pediatr Surg Rep. 2020 Jan;8(1):e112-e116. doi: 10.1055/s-0040-1721054. Epub 2020 Dec 15.
Ruptured giant omphaloceles (GO) and gastroschisis with total liver herniation are rare cases of exceptionally large abdominal wall defects. Many of these children have lethal outcome. The surgical and postsurgical management are complex. We report on two cases treated with staged surgical repair using a wound retractor as a silo. With this technique, the liver and intestines could be reduced into the abdomen with secondary closure of the abdominal cavity within the first 1 to 2 weeks of life.
巨大脐膨出破裂(GO)和伴有全肝疝出的腹裂是腹壁缺损异常大的罕见病例。这些患儿中的许多都有致命结局。手术及术后管理很复杂。我们报告两例采用伤口牵开器作为“储仓”进行分期手术修复的病例。通过这种技术,肝脏和肠道可在出生后的头1至2周内回纳入腹腔,随后二期关闭腹腔。