• 文献检索
  • 文档翻译
  • 深度研究
  • 学术资讯
  • Suppr Zotero 插件Zotero 插件
  • 邀请有礼
  • 套餐&价格
  • 历史记录
应用&插件
Suppr Zotero 插件Zotero 插件浏览器插件Mac 客户端Windows 客户端微信小程序
定价
高级版会员购买积分包购买API积分包
服务
文献检索文档翻译深度研究API 文档MCP 服务
关于我们
关于 Suppr公司介绍联系我们用户协议隐私条款
关注我们

Suppr 超能文献

核心技术专利:CN118964589B侵权必究
粤ICP备2023148730 号-1Suppr @ 2026

文献检索

告别复杂PubMed语法,用中文像聊天一样搜索,搜遍4000万医学文献。AI智能推荐,让科研检索更轻松。

立即免费搜索

文件翻译

保留排版,准确专业,支持PDF/Word/PPT等文件格式,支持 12+语言互译。

免费翻译文档

深度研究

AI帮你快速写综述,25分钟生成高质量综述,智能提取关键信息,辅助科研写作。

立即免费体验

法洛四联症中的罕见相关异常:婴儿中的弯刀综合征。

A Rare Associated Anomaly in Tetralogy of Fallot: Scimitar Syndrome in an Infant.

机构信息

Department of Pediatric Cardiology, Istanbul Mehmet Akif Ersoy Thoracic and Cardiovascular Surgery Center and Research Hospital, Istanbul, Turkey.

出版信息

Braz J Cardiovasc Surg. 2021 Aug 6;36(4):578-580. doi: 10.21470/1678-9741-2020-0185.

DOI:10.21470/1678-9741-2020-0185
PMID:33355797
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC8522306/
Abstract

Pulmonary venous connections may be infrequently abnormal in patients with tetralogy of Fallot (TOF). A special subgroup of partial anomalous pulmonary venous return,"scimitar cyndrome", and its coexistence with TOF is less frequently reported. It may proceed unnoticed, as cyanosis already predominates in the clinical picture. This uncommon association must be kept in mind for patients with TOF who have an accessory flow in the inferior vena cava, especially when all pulmonary venous return to the left atrium is not clearly seen.

摘要

肺静脉连接在法洛四联症(TOF)患者中可能不常出现异常。部分肺静脉异常回流的一个特殊亚组,“弯刀综合征”,及其与 TOF 的共存,报道较少。由于临床上已经存在紫绀,因此可能未被注意到。对于存在下腔静脉附加血流的 TOF 患者,特别是当并非所有肺静脉均回流至左心房时,必须牢记这种不常见的关联。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3d43/8522306/d2b2bcc3dede/rbccv-36-04-0578-g01.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3d43/8522306/d2b2bcc3dede/rbccv-36-04-0578-g01.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3d43/8522306/d2b2bcc3dede/rbccv-36-04-0578-g01.jpg

相似文献

1
A Rare Associated Anomaly in Tetralogy of Fallot: Scimitar Syndrome in an Infant.法洛四联症中的罕见相关异常:婴儿中的弯刀综合征。
Braz J Cardiovasc Surg. 2021 Aug 6;36(4):578-580. doi: 10.21470/1678-9741-2020-0185.
2
Surgical correction of rare anomaly of scimitar syndrome with tetralogy of Fallot.手术矫正弯刀综合征合并法洛四联症的罕见异常。
J Card Surg. 2021 Jun;36(6):2130-2132. doi: 10.1111/jocs.15429. Epub 2021 Feb 14.
3
Superior sinus venosus defect with partial anomalous pulmonary venous return in a patient with tetralogy of Fallot.法洛四联症患者合并上腔静脉缺损及部分性肺静脉异位引流。
J Card Surg. 2022 Nov;37(11):3889-3891. doi: 10.1111/jocs.16806. Epub 2022 Jul 28.
4
[A case of partial anomalous pulmonary venous return to inferior vena cava and left atrium (Scimitar syndrome)].[一例部分性肺静脉异常回流至下腔静脉及左心房(镰刀综合征)]
Nihon Kyobu Geka Gakkai Zasshi. 1994 Jan;42(1):144-9.
5
Tetralogy of Fallot associated with a rare type partially anomalous pulmonary venous connection and levoatrial cardinal vein.法洛四联症合并一种罕见类型的部分性肺静脉异位连接及左位心房总静脉。
J Card Surg. 2022 Nov;37(11):3943-3946. doi: 10.1111/jocs.16825. Epub 2022 Aug 2.
6
Scimitar sign with normal pulmonary venous drainage and anomalous inferior vena cava.伴有正常肺静脉引流和下腔静脉异常的弯刀征。
Thorax. 1988 Aug;43(8):651-2. doi: 10.1136/thx.43.8.651.
7
Transcatheter therapy in partially abnormal pulmonary venous return with additional drainage to the left atrium.经导管治疗部分异常肺静脉回流并伴有额外的左心房引流。
Int J Cardiol. 2013 Dec 10;170(2):221-6. doi: 10.1016/j.ijcard.2013.10.061. Epub 2013 Oct 30.
8
[A rare cause of recurrent wheezing and respiratory distress: Scimitar syndrome].[反复喘息和呼吸窘迫的罕见病因:弯刀综合征]
Turk Kardiyol Dern Ars. 2011 Oct;39(7):595-8. doi: 10.5543/tkda.2011.01581.
9
Isolated Anomalous Right Superior Pulmonary Venous Return to the Inferior Vena Cava.孤立性右肺上静脉异常回流至下腔静脉。
World J Pediatr Congenit Heart Surg. 2022 Jul;13(4):508-509. doi: 10.1177/21501351221098596.
10
Rare associations of tetralogy of Fallot with anomalous left coronary artery from pulmonary artery and totally anomalous pulmonary venous connection.法洛四联症与源自肺动脉的异常左冠状动脉及完全性肺静脉异位连接的罕见关联。
Cardiol Young. 2016 Jun;26(5):1017-20. doi: 10.1017/S1047951116000342. Epub 2016 Apr 8.

引用本文的文献

1
A bleeding sword: Scimitar syndrome in a child with hematemesis due to esophageal varices - a case report.一把带血的剑:一名因食管静脉曲张呕血的儿童的弯刀综合征——病例报告
Ann Med Surg (Lond). 2025 Jan 31;87(2):1013-1016. doi: 10.1097/MS9.0000000000002879. eCollection 2025 Feb.

本文引用的文献

1
Tetralogy of Fallot with total anomalous pulmonary venous drainage.
Ann Thorac Surg. 2008 Dec;86(6):1937-40. doi: 10.1016/j.athoracsur.2008.07.093.
2
A case series of five infants with scimitar syndrome.一例包含五名患有弯刀综合征婴儿的病例系列。
Adv Neonatal Care. 2003 Jun;3(3):121-32. doi: 10.1016/s1536-0903(03)00106-1.
3
Tetralogy of Fallot associated with scimitar syndrome.法洛四联症合并弯刀综合征。
Cardiol Young. 2000 Jan;10(1):70-2. doi: 10.1017/s1047951100006454.
4
Scimitar syndrome in infancy.婴儿期弯刀综合征
J Am Coll Cardiol. 1993 Sep;22(3):873-82. doi: 10.1016/0735-1097(93)90206-g.
5
Tetralogy of Fallot with anomalous pulmonary venous connections: a rare but clinically important association.法洛四联症合并肺静脉连接异常:一种罕见但具有临床重要性的关联。
Br Heart J. 1990 Nov;64(5):325-8. doi: 10.1136/hrt.64.5.325.