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经皮球囊阻断逆行经静脉栓塞术成功治疗先天性肝外门体分流的 1 例成人病例。

An Adult Case of Congenital Extrahepatic Portosystemic Shunt Successfully Treated with Balloon-occluded Retrograde Transvenous Obliteration.

机构信息

Department of Gastroenterology and Oncology, Tokushima University Graduate School of Biomedical Sciences, Japan.

Department of Cardiovascular Medicine, Tokushima University Graduate School of Biomedical Sciences, Japan.

出版信息

Intern Med. 2021 Jun 15;60(12):1839-1845. doi: 10.2169/internalmedicine.5914-20. Epub 2021 Jan 15.

DOI:10.2169/internalmedicine.5914-20
PMID:33456037
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC8263181/
Abstract

A 42-year-old woman visited our hospital due to syncope. Contrast-enhanced CT revealed portosystemic shunt, portal vein hypoplasia, and multiple liver nodules. The histological examination of a liver biopsy specimen exhibited portal vein hypoplasia and revealed that the liver tumor was positive for glutamine synthetase. The patient was therefore diagnosed with congenital extrahepatic portosystemic shunt type II, and with focal nodular hyperplasia (FNH)-like nodules. She had the complication of severe portopulmonary hypertension and underwent complete shunt closure by balloon-occluded retrograde transvenous obliteration (B-RTO). The intrahepatic portal vein was well developed at 1 year after B-RTO, and multiple liver nodules completely regressed. Her pulmonary hypertension also improved.

摘要

一位 42 岁女性因晕厥就诊于我院。增强 CT 显示门腔静脉分流、门静脉发育不良和多个肝脏结节。肝脏活检组织学检查显示门静脉发育不良，并发现肝肿瘤谷氨酸合成酶阳性。因此，该患者被诊断为先天性肝外门腔静脉分流 II 型，伴局灶性结节性增生（FNH）样结节。该患者并发严重的门肺高血压，并接受了球囊阻断逆行经静脉闭塞（B-RTO）以完全关闭分流。B-RTO 后 1 年，肝内门静脉发育良好，多个肝脏结节完全消退，其高血压也有所改善。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/9ad0/8263181/4dafa2d2d23c/1349-7235-60-1839-g007.jpg
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https://cdn.ncbi.nlm.nih.gov/pmc/blobs/9ad0/8263181/4dafa2d2d23c/1349-7235-60-1839-g007.jpg

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