类同纵向广泛横贯性脊髓炎的福-阿二氏综合征
Foix-Alajouanine Syndrome Mimicking Longitudinally Extensive Transverse Myelitis.
作者信息
Rathnam Anirudha S, Memon Anza B
机构信息
Department of Neurology, Henry Ford Health System, Detroit, Michigan, USA.
Wayne State University, School of Medicine, Detroit, Michigan, USA.
出版信息
Eur J Case Rep Intern Med. 2020 Nov 10;7(12):002063. doi: 10.12890/2020_002063. eCollection 2020.
UNLABELLED
Foix-Alajouanine syndrome is an arteriovenous malformation causing subacute congestive myelopathy that can lead to progressive paraplegia. It typically affects the lower thoracic and lumbosacral levels. Arteriovenous fistula (AVF) leads to increased venous pressure, decreasing the arteriovenous pressure gradient and leading to a decrease in spinal cord perfusion, oedema and necrosis. Early recognition and surgical intervention can result in a good prognosis.
LEARNING POINTS
Spinodural arteriovenous fistula (SDAF) can present with longitudinally extensive transverse myelitis (LETM), progressive gait instability, and lower extremity weakness.Failure to promptly recognize this condition and misdiagnosis can result in a poor outcome.Microsurgical obliteration of the SDAF provides better results than embolization.
未标注
福瓦-阿亚吉综合征是一种动静脉畸形，可导致亚急性充血性脊髓病，进而引发进行性截瘫。它通常影响下胸段和腰骶段。动静脉瘘（AVF）会导致静脉压升高，动静脉压力梯度降低，从而导致脊髓灌注减少、水肿和坏死。早期识别和手术干预可带来良好预后。
学习要点
硬脊膜动静脉瘘（SDAF）可表现为纵向广泛横贯性脊髓炎（LETM）、进行性步态不稳和下肢无力。未能及时识别这种情况以及误诊会导致不良后果。SDAF的显微手术闭塞比栓塞效果更好。
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