Sadighi Nahid, Tajmalzai Abasin, Salahshour Faeze
Department of Radiology, Tehran University of Medical Sciences, Tehran, Iran.
Department of Radiology, Kabul University of Medical Sciences, Kabul, Afghanistan.
Radiol Case Rep. 2021 Jun 12;16(8):2187-2191. doi: 10.1016/j.radcr.2021.05.048. eCollection 2021 Aug.
Foix-Alajouanine syndrome is a rare progressive form of spinal AVM predominantly affecting the lower thoracic and/or lumbosacral regions. This study aims to describe the imaging findings of spinal AVM causing Foix-Alajouanine syndrome and to review the literature. We present a 48-year-old man with progressive back pain, leg weakness, and gait imbalance without urinary retention. We discuss the clinical and imaging findings and the significance of MRI in establishing the diagnosis. A definitive diagnosis of spinal AVM requires radiographic demonstration of the vascular anomaly. Despite the high sensitivity of angiography for the diagnosis of spinal AVM, the result of the study may be inconclusive and/or negative. The key MRI findings are the presence of abnormally dilated perimedullary vessels with signal voids from a high-velocity flow on T1 and T2 weighted images.
福-阿二氏综合征是一种罕见的进行性脊髓动静脉畸形，主要累及下胸段和/或腰骶部区域。本研究旨在描述导致福-阿二氏综合征的脊髓动静脉畸形的影像学表现并复习相关文献。我们报告一名48岁男性，有进行性背痛、腿部无力和步态失衡，但无尿潴留。我们讨论了临床和影像学表现以及MRI在确立诊断中的意义。脊髓动静脉畸形的明确诊断需要通过影像学检查证实血管异常。尽管血管造影对脊髓动静脉畸形的诊断具有较高的敏感性，但研究结果可能不明确和/或为阴性。MRI的关键表现是在T1加权和T2加权图像上，髓周血管异常扩张并伴有高速血流形成的信号缺失。
