Medicine Based Department, Faculty of Medicine and Health Science, University of Malaysia Sabah, Kota Kinabalu, Sabah, Malaysia.
Department of General Medicine, Queen Elizabeth Hospital, Kota Kinabalu, Sabah, Malaysia.
Am J Case Rep. 2021 Jan 20;22:e928419. doi: 10.12659/AJCR.928419.
BACKGROUND Myasthenic crisis is a condition characterized by the sudden onset of myasthenic weakness involving the respiratory muscles and requires ventilatory support to prevent death. This is a case report of respiratory failure in a 43-year-old man as the first presentation of myasthenia gravis. CASE REPORT A 43-year-old man with underlying hypertension and a lacunar stroke with good muscle-power recovery presented with severe community-acquired pneumonia, complicated with respiratory failure requiring invasive ventilatory support. He responded well to the intravenous antibiotic therapy and after 1 week of treatment, he was hemodynamically stable and his septic parameters improved. However, he persistently failed to maintain adequate spontaneous respiratory effort after the removal of the ventilatory support and had to be reintubated multiple times. There was no other identifiable cause for the worsening respiratory failure. He had no clinical features or muscle weakness suggestive of myasthenia gravis. However, his blood test was positive for serum anti-acetylcholine receptor antibodies and repetitive nerve stimulation tests showed the characteristic decremental response of compound muscle action potential amplitude, in keeping with the diagnosis of myasthenia gravis. He responded well to intravenous immunoglobulin and was discharged with anticholinesterase inhibitors and long-term immunosuppression therapy. CONCLUSIONS This report demonstrates that when patients are admitted to the hospital with acute respiratory failure without any underlying pulmonary disease and with weakness of the respiratory muscles, the diagnosis of myasthenia gravis presenting with a myasthenic crisis should be considered.
肌无力危象是一种以呼吸肌突然出现肌无力为特征的疾病,需要呼吸支持以防止死亡。这是一例以重症肌无力为首发表现的 43 岁男性呼吸衰竭病例报告。
一名 43 岁男子,有高血压和腔隙性中风病史,肌肉力量恢复良好,因社区获得性肺炎严重,并发呼吸衰竭,需要有创通气支持。他对静脉抗生素治疗反应良好,经过 1 周的治疗,他血流动力学稳定,感染参数改善。然而,在去除通气支持后,他始终无法维持足够的自主呼吸努力,多次需要重新插管。没有其他可识别的原因导致呼吸衰竭恶化。他没有提示重症肌无力的临床特征或肌肉无力。然而,他的血清抗乙酰胆碱受体抗体检测呈阳性,重复神经刺激试验显示复合肌肉动作电位幅度的特征性递减反应,符合重症肌无力的诊断。他对静脉注射免疫球蛋白反应良好,出院时给予抗胆碱酯酶抑制剂和长期免疫抑制治疗。
本报告表明,当患者因无基础肺部疾病且呼吸肌无力而入院急性呼吸衰竭时,应考虑诊断为以肌无力危象为表现的重症肌无力。