巨大右心室黏液瘤表现为右心衰竭伴全身淤血：一例罕见病例报告。
Giant right ventricular myxoma presenting as right heart failure with systemic congestion: a rare case report.
作者信息
Lu Chen, Yang Peng, Hu Jia
机构信息
Department of Cardiovascular Surgery, West China Hospital, Sichuan University, No.37 Guoxue Alley, Wuhou District, Chengdu, 610041, Sichuan Province, People's Republic of China.
出版信息
BMC Surg. 2021 Jan 29;21(1):64. doi: 10.1186/s12893-020-00977-4.
BACKGROUND
Myxoma is an uncommon disease and its symptoms vary greatly depending on size, location and mobility. Right-sided myxoma, especially right ventricular myxoma, is much rarer, and the symptoms are alien and uncharacteristic. The lack of understandings poses challenges to prompt diagnosis and timely treatment.
CASE PRESENTATION
A 44-year-old female patient was diagnosed with giant right ventricular tumor. Right heart failure and systemic congestion caused by right ventricular outflow tract obstruction were observed on this case. Surgery was performed to excise the mass which was measured at 9.5 * 5.0 cm and confirmed as myxoma pathologically.
CONCLUSIONS
Right-side myxoma is easy to be unnoticed due to its low incident rate and atypical symptoms. Delay in surgical intervention might cause unrecoverable complications. More comprehensive understanding of the symptoms is expected to help improving the diagnose and treat of right-sided myxoma.
背景
黏液瘤是一种罕见疾病，其症状因大小、位置和活动度的不同而有很大差异。右侧黏液瘤，尤其是右心室黏液瘤更为罕见，其症状奇特且不典型。对其认识不足给及时诊断和治疗带来了挑战。
病例介绍
一名44岁女性患者被诊断为巨大右心室肿瘤。该病例中观察到由右心室流出道梗阻引起的右心衰竭和全身充血。手术切除了肿块，其大小为9.5×5.0厘米，病理证实为黏液瘤。
结论
右侧黏液瘤由于发病率低且症状不典型，容易被忽视。手术干预延迟可能导致无法恢复的并发症。对症状有更全面的了解有望有助于改善右侧黏液瘤的诊断和治疗。
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