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全索状室管膜下巨细胞型室管膜瘤:一例表现异常、组织学诊断具有挑战性且行一期肿瘤完整切除的有趣病例

Holocord Tanycytic Ependymoma: An Interesting Case with Unusual Presentation, Challenging Histological Diagnosis, and Single-staged Complete Tumor Resection.

作者信息

Sankhla Suresh K, Khan Ghulam M

机构信息

Department of Neurosurgery, Global Hospital, Mumbai, India.

出版信息

J Pediatr Neurosci. 2020 Jul-Sep;15(3):183-189. doi: 10.4103/jpn.JPN_100_19. Epub 2020 Nov 6.

DOI:10.4103/jpn.JPN_100_19
PMID:33531930
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC7847113/
Abstract

An interesting case of intramedullary holocord cystic tumor in an 11-year old boy is reported, who presented with unusual clinical manifestations and radiological features. Gross total resection of the tumor was performed in a single-staged surgery. A rare combination of unusual presentation, uncommon histopathological findings, and challenges in the selection of surgical options were discussed with a detailed review of the literature.

摘要

报告了一例11岁男孩的髓内全脊髓囊性肿瘤病例,该病例具有不寻常的临床表现和影像学特征。肿瘤在一期手术中实现了全切。本文结合文献详细讨论了该病例不寻常的表现、罕见的组织病理学发现以及手术方案选择方面的挑战。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/e796/7847113/32872df3e7b3/JPN-15-183-g004.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/e796/7847113/a557fe9c4fdf/JPN-15-183-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/e796/7847113/6e456b01b10e/JPN-15-183-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/e796/7847113/77fa93d0f194/JPN-15-183-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/e796/7847113/32872df3e7b3/JPN-15-183-g004.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/e796/7847113/a557fe9c4fdf/JPN-15-183-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/e796/7847113/6e456b01b10e/JPN-15-183-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/e796/7847113/77fa93d0f194/JPN-15-183-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/e796/7847113/32872df3e7b3/JPN-15-183-g004.jpg

相似文献

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Holocord Tanycytic Ependymoma: An Interesting Case with Unusual Presentation, Challenging Histological Diagnosis, and Single-staged Complete Tumor Resection.全索状室管膜下巨细胞型室管膜瘤:一例表现异常、组织学诊断具有挑战性且行一期肿瘤完整切除的有趣病例
J Pediatr Neurosci. 2020 Jul-Sep;15(3):183-189. doi: 10.4103/jpn.JPN_100_19. Epub 2020 Nov 6.
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本文引用的文献

1
Single staged complete length excision of the holocord ependymoma: Team work.全脊髓室管膜瘤的单阶段全长切除:团队协作。
J Pediatr Neurosci. 2015 Oct-Dec;10(4):396-8. doi: 10.4103/1817-1745.174450.
2
Tanycytic ependymoma: a challenging histological diagnosis.室管膜下巨细胞星形细胞瘤:一种具有挑战性的组织学诊断。
Case Rep Neurol Med. 2013;2013:170791. doi: 10.1155/2013/170791. Epub 2013 Feb 14.
3
Holocord ependymoma.全脊髓室管膜瘤
Turk Neurosurg. 2012;22(2):250-3. doi: 10.5137/1019-5149.JTN.3281-10.1.
4
Holocord pilocytic astrocytoma--case report and review of the literature.全脊髓毛细胞型星形细胞瘤——病例报告及文献复习
Clin Neurol Neurosurg. 2009 Feb;111(2):203-7. doi: 10.1016/j.clineuro.2008.09.014. Epub 2008 Nov 5.
5
Intramedullary spinal ependymomas: analysis of a consecutive series of 82 adult cases with particular attention to patients with no preoperative neurological deficit.脊髓髓内室管膜瘤:对连续82例成年病例的分析,特别关注术前无神经功能缺损的患者。
Neurosurgery. 2008 Jun;62(6):1279-85; discussion 1285-6. doi: 10.1227/01.neu.0000333299.26566.15.
6
Surgical management of long intramedullary spinal cord tumors.长节段脊髓髓内肿瘤的外科治疗
Childs Nerv Syst. 2008 Feb;24(2):219-23. doi: 10.1007/s00381-007-0405-7. Epub 2007 Jul 18.
7
Motor-evoked potential monitoring for intramedullary spinal cord tumor surgery: correlation of clinical and neurophysiological data in a series of 100 consecutive procedures.髓内脊髓肿瘤手术中的运动诱发电位监测:100例连续手术的临床与神经生理学数据相关性研究
Neurosurg Focus. 1998 May 15;4(5):e1. doi: 10.3171/foc.1998.4.5.4.
8
Surgical treatment of intramedullary spinal cord ependymomas: can outcome be predicted by tumor parameters?脊髓髓内室管膜瘤的外科治疗:肿瘤参数能否预测预后?
J Spinal Disord Tech. 2004 Dec;17(6):516-21. doi: 10.1097/01.bsd.0000129585.91599.5c.
9
Intraoperative diagnosis of tanycytic ependymoma: pitfalls and differential diagnosis.室管膜瘤的术中诊断:陷阱与鉴别诊断
Diagn Cytopathol. 2001 Apr;24(4):289-92. doi: 10.1002/dc.1061.
10
Spinal tanycytic ependymomas.脊髓室管膜下巨细胞型室管膜瘤。
Acta Neuropathol. 2001 Jan;101(1):43-8. doi: 10.1007/s004010000265.