Department of Cardiovascular Surgery, Faculty of Medicine, Acibadem Mehmet Ali Aydinlar University, Istanbul, Turkey.
Braz J Cardiovasc Surg. 2021 Feb 1;36(1):133-136. doi: 10.21470/1678-9741-2019-0228.
Infantile scimitar syndrome (SS) is a rare congenital heart disease and has high mortality. Guidelines have not been established, but surgery is indicated in symptomatic patients. Despite the various surgical approaches, outcomes continue to be disappointing. We present our surgical experience with an infantile SS patient who had stenotic pulmonary veins contralateral to the hypoplastic lung with complicated anatomy. There are few cases with this complex pathology in the literature. Moreover, our patient was the first transplant-free survivor with this complexity in the literature.
婴儿镰刀综合征（SS）是一种罕见的先天性心脏病，死亡率高。虽然指南尚未建立，但有症状的患者需要手术。尽管有多种手术方法，但结果仍不尽如人意。我们报告了一例患有婴儿 SS 患者的手术经验，该患者存在肺静脉狭窄，而对侧肺发育不良，且解剖结构复杂。文献中很少有这种复杂病理的病例。此外，我们的患者是该复杂性文献中首例无移植幸存者。
