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骨髓增生异常/骨髓增殖性肿瘤所致母细胞样浆细胞样树突状细胞肿瘤诱导治疗期间的严重肿瘤溶解综合征。

Severe tumor lysis syndrome during the induction therapy for the treatment of blastic plasmacytoid dendritic cell neoplasm arising from myelodysplastic/myeloproliferative neoplasms.

作者信息

Sagou Ken, Ito Makoto, Kawamura Yuma, Ukai Shun, Goto Miyo, Fukushima Nobuaki, Ozeki Kazutaka, Fukuyama Ryuichi, Kohno Akio

机构信息

Department of Hematology and Oncology JA Aichi Konan Kosei Hospital Aichi Japan.

Department of Hematology and Oncology Nagoya University Graduate School of Medicine Aichi Japan.

出版信息

Clin Case Rep. 2020 Dec 20;9(2):878-882. doi: 10.1002/ccr3.3690. eCollection 2021 Feb.

Abstract

BPDCN shows clinically heterogeneous characteristics. And as other hematological malignancies, symptoms of BPDCN suggesting a high tumor burden, such as high white blood cell count or splenomegaly, should be carefully considered to prevent TLS.

摘要

母细胞性浆细胞样树突状细胞肿瘤(BPDCN)具有临床异质性特征。与其他血液系统恶性肿瘤一样,对于提示高肿瘤负荷的BPDCN症状,如高白细胞计数或脾肿大,应仔细考虑以预防肿瘤溶解综合征(TLS)。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/77d2/7869312/cc05ce2e6529/CCR3-9-878-g001.jpg

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