Goswami Mridula, Pandian Ramanandvignesh, Sharma Sadhna
Department of Pedodontics and Preventive Dentistry, Maulana Azad Institute of Dental Sciences, New Delhi, India.
Int J Clin Pediatr Dent. 2020 Sep-Oct;13(5):566-568. doi: 10.5005/jp-journals-10005-1790.
Moyamoya disease (MMD) is a rare neurovascular disorder that is characterized by chronic progressive stenosis at the apices and bilateral occlusion of the intracranial internal carotid arteries. The occlusion is gradual in manner; multiple anastomoses are formed between the internal and external carotid arteries. The incidence of MMD has increased in Asian countries with a decline in Europe and United States.
The case report describes the specific clinical features and dental treatment in a 12-year-old male presenting with MMD with right-side hemiplegia. The patient presented with broken tooth in the upper front tooth region due to trauma. The dental treatment plan focused on providing restorative as well as preventive care to the patient.
The patients with MMD have an increased risk of stroke development, which may be aggravated by pain or anxiety. It is necessary to avoid cerebral ischemic attacks caused by fluctuating BP and respiration. It becomes imperative to maintain normocapnia, normotension, and pain control during the procedure in order to prevent postoperative ischemic complications. Dental professionals must attain a complete knowledge of this disease and perform the dental treatment in pain and stress-free manner.
Goswami M, Pandian R, Sharma S. Moyamoya Disease-"A Puff of Smoke": A Rare Pediatric Case Report. Int J Clin Pediatr Dent 2020;13(5):566-568.
烟雾病（MMD）是一种罕见的神经血管疾病，其特征是颅内颈内动脉顶端慢性进行性狭窄及双侧闭塞。闭塞呈渐进性；颈内动脉和颈外动脉之间形成多个吻合支。烟雾病的发病率在亚洲国家有所上升，而在欧洲和美国则有所下降。
该病例报告描述了一名12岁患有烟雾病并伴有右侧偏瘫男性的具体临床特征及牙科治疗情况。患者因外伤导致上前牙区牙齿折断。牙科治疗计划侧重于为患者提供修复及预防性护理。
烟雾病患者发生中风的风险增加，疼痛或焦虑可能会加重这种风险。有必要避免因血压和呼吸波动引起的脑缺血发作。为防止术后缺血性并发症，在手术过程中保持正常碳酸血症、正常血压及控制疼痛至关重要。牙科专业人员必须全面了解这种疾病，并以无痛、无压力的方式进行牙科治疗。
戈斯瓦米M，潘迪安R，夏尔马S。烟雾病——“一缕烟雾”：一例罕见的儿科病例报告。《国际临床儿科牙科学杂志》2020年；13（5）：566 - 568。
