Lim Hui Jun, Tan Joey Wee-Shan, Chia Claramae Shulyn, Ong Chin-Ann Johnny
Department of Sarcoma, Peritoneal and Rare Tumours (SPRinT), Division of Surgery and Surgical Oncology, National Cancer Centre Singapore, Singapore.
J Surg Case Rep. 2021 Feb 28;2021(2):rjaa610. doi: 10.1093/jscr/rjaa610. eCollection 2021 Feb.
Retroperitoneal lymphangioma is an uncommon and benign mesodermal tumour that arises from the retroperitoneal lymphatics. Notably, it is a rare occurrence in adults, where <200 adult retroperitoneal lymphangioma cases have been published in the literature. Additionally, retroperitoneal lymphangioma is often difficult to diagnose preoperatively and formal diagnosis is frequently determined following surgical exploration. Here, we describe a rare case of retroperitoneal lymphangioma in a 74-year-old man who presented with a 6-month history of intermittent fresh per rectal bleeding with an incidental non-tender left iliac fossa firm mass on examination. Computed tomography scan established a retroperitoneal cystic lesion abutting the aorta and left common iliac vessels. Surgical exploration revealed a large cystic mass and a clean plane of dissection was performed, where the mass was completely excised with all the key structures preserved. Histology was consistent with a retroperitoneal lymphangioma.
腹膜后淋巴管瘤是一种罕见的良性中胚层肿瘤,起源于腹膜后淋巴管。值得注意的是,它在成年人中很少见,文献中报道的成人腹膜后淋巴管瘤病例不到200例。此外,腹膜后淋巴管瘤术前常难以诊断,通常在手术探查后才能确定正式诊断。在此,我们描述一例罕见的74岁男性腹膜后淋巴管瘤病例,该患者有6个月间歇性新鲜直肠出血病史,检查时偶然发现左髂窝有一个无压痛的实性肿块。计算机断层扫描显示一个腹膜后囊性病变,毗邻主动脉和左髂总血管。手术探查发现一个大的囊性肿块,并进行了清晰的分离平面,在保留所有关键结构的情况下将肿块完全切除。组织学检查结果与腹膜后淋巴管瘤一致。