Deiana Giuseppe, Genadiev Genadi, Giordano Antonio Nicola, Moro Mario, Spanu Francesco, Urru Flavia, Camparini Stefano
Department of Vascular Surgery, Brotzu Hospital, Cagliari, Italy.
Vasc Specialist Int. 2021 Mar 31;37(1):46-49. doi: 10.5758/vsi.200083.
Primary malignant aortic tumors are rare and aggressive. Most cases are diagnosed at advanced stages or during autopsies with a median overall survival of 8 months from diagnosis. We present the case of a 59-year-old male with angiosarcoma involving all segments of the thoracic aorta and a large floating thrombus causing acute mesenteric ischemia, which was treated successfully with embolectomy. Graft replacement of the aorta should be considered in cases of localized disease and when patients are fit for surgery. The best medical and surgical treatment remains unclear, and further studies are needed.
原发性恶性主动脉肿瘤罕见且侵袭性强。大多数病例在晚期或尸检时被诊断出来，从诊断起的中位总生存期为8个月。我们报告了一例59岁男性血管肉瘤累及胸主动脉各段并伴有巨大漂浮血栓导致急性肠系膜缺血的病例，该病例通过栓子切除术成功治疗。对于局限性疾病且患者适合手术的情况，应考虑进行主动脉移植置换术。最佳的药物和手术治疗仍不明确，需要进一步研究。
