Faculty of Medicine, Department of Obstetrics and Gynecology, Dicle University, Diyarbakır, Turkey.
Acta Chir Belg. 2022 Aug;122(4):275-278. doi: 10.1080/00015458.2021.1911096. Epub 2021 Apr 9.
One of the least common forms of Müllerian anomalies is Herlyn-Werner-Wunderlich syndrome (HWWS), characterized by uterus didelphys, obstructed hemi-vagina, and ipsilateral renal agenesis (OHVIRA). HWWS is also known as OHVIRA syndrome. Patients with OHVIRA syndrome generally present with increasing pelvic pain, dysmenorrhoea, and pelvic mass during puberty, shortly after menarche. These patients may be treated successfully with a minimally invasive method.
We present three previously asymptomatic patients with OHVIRA syndrome who presented with acute abdomen shortly after menarche. These patients were treated with a minimally invasive method.
Patients with OHVIRA syndrome may be treated with minimally invasive method after definitive diagnosis and, laparoscopy and laparotomy should be avoided as much as possible. Minimally invasive treatment modality is not only cost-effective, but also provides symptomatic relief and preserves fertility.
Müllerian 异常中最不常见的形式之一是 Herlyn-Werner-Wunderlich 综合征（HWWS），其特征为双子宫、单侧阴道闭锁和同侧肾发育不全（OHVIRA）。HWWS 也称为 OHVIRA 综合征。OHVIRA 综合征患者通常在青春期初潮后不久出现进行性盆腔疼痛、痛经和盆腔肿块。这些患者可以通过微创方法成功治疗。
我们报告了 3 例之前无症状的 OHVIRA 综合征患者，她们在初潮后不久出现了急性腹痛。这些患者采用微创方法进行了治疗。
OHVIRA 综合征患者在明确诊断后可以采用微创方法进行治疗，应尽可能避免腹腔镜和剖腹术。微创治疗方式不仅具有成本效益，还能缓解症状并保留生育能力。
