Tuqan Anas R, Salahaldin Rayan R, Abubaker Mais E, Zaben Basel A, Barabrah Anas M, Rayyan Mohammad H, Jaber Saadeh S
Faculty of medicine, Al-Quds university, Jerusalem, Palestine.
Department of Obstetrics and Gynecology, AL-Makassed Charitable Society Hospital, East Jerusalem, Palestine.
Case Rep Womens Health. 2024 Aug 23;43:e00647. doi: 10.1016/j.crwh.2024.e00647. eCollection 2024 Oct.
Herlyn-Werner-Wunderlich (HWW) syndrome is a rare congenital condition characterized by renal agenesis, uterine didelphys, and obstructed hemivagina. This report presents the case of a 19-year-old woman who reported lower abdominal pain and offensive vaginal discharge. Imaging revealed a didelphys uterus, two vaginas, two cervixes, hematocolpos, and an absent right kidney. Surgical intervention involved draining the hematocolpos and excising the uterine septum. After surgery, the patient successfully conceived and had a full-term pregnancy, delivering via cesarean section without complications. This case highlights the importance of early diagnosis and surgical management in preventing complications such as endometriosis and infertility. Prompt recognition and treatment are crucial for preserving fertility in patients with HWW syndrome.
赫林-韦纳-温德利希（HWW）综合征是一种罕见的先天性疾病，其特征为肾缺如、双子宫和阴道半段梗阻。本报告介绍了一名19岁女性的病例，该女性自述下腹部疼痛且阴道有异味分泌物。影像学检查显示为双子宫、双阴道、双宫颈、阴道积血以及右肾缺如。手术干预包括引流阴道积血和切除子宫纵隔。术后，患者成功受孕并足月妊娠，通过剖宫产分娩，未出现并发症。该病例强调了早期诊断和手术管理对于预防诸如子宫内膜异位症和不孕症等并发症的重要性。及时识别和治疗对于保留HWW综合征患者的生育能力至关重要。
