Agrawal Shashank, Patil Abhijit, Singh Abhishek Gajendra, Ganpule Arvind Prakash, Sabnis Ravindra Bhalchandra, Desai Mahesh Ramanlal
Department of Urology, Muljibhai Patel Urological Hospital, Nadiad, Gujarat, India.
Int J Appl Basic Med Res. 2021 Jan-Mar;11(1):60-62. doi: 10.4103/ijabmr.IJABMR_341_20. Epub 2021 Jan 26.
Myelolipoma of the kidney is a very rare benign disease which is composed of mature adipose tissue admixed with mature hematopoietic elements in varying proportions. The most common location of myelolipoma is in the adrenal glands, but extra-adrenal myelolipomas in other locations such as the retroperitoneum, presacral region, pelvis, and mediastinum has also been reported. In this case report, we present a case of huge extra-adrenal myelolipoma in renal parenchyma which is rare site for its origin. We report a case of extra-adrenal myelolipoma occurring in the left kidney of a 46-year-old Indian man. We describe the radiological and clinicopathologic features of this unusual tumor with a review of the literature. This case is noteworthy because the tumor was very enlarged and its site was unusual. It is generally impossible to distinguish extra-adrenal myelolipoma from other retroperitoneal tumors by radiological imaging given the rarity of tumor more cases need to be reported to elucidate its biological behavior.
肾髓质脂肪瘤是一种非常罕见的良性疾病，由成熟的脂肪组织与不同比例的成熟造血成分混合而成。髓质脂肪瘤最常见的部位是肾上腺，但也有报道称其可发生于其他部位的肾上腺外髓质脂肪瘤，如腹膜后、骶前区、骨盆和纵隔。在本病例报告中，我们呈现了一例发生于肾实质的巨大肾上腺外髓质脂肪瘤，其起源部位罕见。我们报告了一例发生在一名46岁印度男性左肾的肾上腺外髓质脂肪瘤。我们描述了这种不寻常肿瘤的放射学和临床病理特征，并对文献进行了回顾。该病例值得注意，因为肿瘤非常大且部位不寻常。鉴于肿瘤的罕见性，通过放射学成像通常无法将肾上腺外髓质脂肪瘤与其他腹膜后肿瘤区分开来，需要报告更多病例以阐明其生物学行为。
