Baio Raffaele, Spiezia Nicola, Schettini Manlio
Department of Urology, University of Salerno, I-84081 Salerno, Italy.
Department of Urology, Lourdes Clinic, I-80040 Massa di Somma, Italy.
Mol Clin Oncol. 2021 Jun;14(6):109. doi: 10.3892/mco.2021.2271. Epub 2021 Mar 23.
Multilocular cystic nephroma is a rare benign kidney tumor, which is typically characterized by a unilateral, multicystic renal mass without solid elements. Cystic nephroma has a bimodal distribution and two-thirds of tumors involve children aged between 3 months and 2 years, with male predominance; a second peak affects the age group >30 years old, in which females are predominantly affected. The incidence rate for this rare tumor in patients aged 5-30 years is only 5%. The present study reports a case of a 31-year-old woman affected by a multilocular cystic nephroma in the upper pole of the right kidney, with direct tumor extension into the renal pelvis through a calyx. After a partial nephrectomy on the patient, the pathological examination confirmed a multilocular cystic nephroma in the right renal specimens.
多房性囊性肾瘤是一种罕见的良性肾肿瘤，其典型特征为单侧多房性肾肿块，无实性成分。囊性肾瘤具有双峰分布，三分之二的肿瘤发生于3个月至2岁的儿童，男性居多；第二个高峰影响年龄大于30岁的人群，其中女性受影响为主。5至30岁患者中这种罕见肿瘤的发病率仅为5%。本研究报告了一例31岁女性，其右肾上极患有多房性囊性肾瘤，肿瘤通过肾盏直接延伸至肾盂。对该患者进行部分肾切除术后，病理检查证实右肾标本为多房性囊性肾瘤。
