Department of Dermatology, Hospital General Universitario de Ciudad Real, Ciudad Real.
Dermatol Online J. 2021 Mar 15;27(3):13030/qt71g4k3qf.
Scleredema adultorum of Buschke is a rare skin disease characterized by skin thickening and tightening typically at the neck and the upper part of the body. This thickening results from increased mucin deposition in the reticular dermis. Three variants are recognized. Scleredema diabeticorum is one subtype associated with diabetes mellitus. We report a man with a history of poorly controlled diabetes presenting with extensive scleredema adultorum of the trunk in a "cuirasse" pattern associated with restrictive lung disease. Cutaneous ultrasonography revealed a marked thickening of the dermis as well as various echogenic spots in the dermis. Cutaneous hardness secondary to scleredema may cause limited mobility. Therefore, respiratory manifestations may be associated and assessed, mainly in cases of extensive scleredema involving trunk and shoulders. Moreover, cutaneous ultrasonography may be useful to monitor the evolution of scleredema and confirm the diagnosis.
成人硬肿病 Buschke 是一种罕见的皮肤疾病,其特征为皮肤增厚和紧绷,通常发生在颈部和上半身。这种增厚是由于网状真皮中黏蛋白沉积增加所致。该病有三种公认的变异型。糖尿病性硬肿病是与糖尿病相关的一种亚型。我们报告了 1 例既往控制不佳的糖尿病患者,其躯干广泛出现“胸甲样”成人硬肿病,伴限制性肺病。皮肤超声显示真皮明显增厚,并在真皮中有各种点状强回声。硬肿病引起的皮肤硬度可能导致活动受限。因此,可能会出现相关的呼吸表现,并进行评估,主要是在累及躯干和肩部的广泛硬肿病的情况下。此外,皮肤超声检查可能有助于监测硬肿病的演变并确认诊断。