Martin Benjamin, Ali Sana, McGuirk Simon P, Chandran Harish
Department of Paediatric Surgery and Urology, Birmingham Children's Hospital, Steelhouse Lane, Birmingham B4 6NH, UK.
Department of Radiology, Birmingham Children's Hospital, Steelhouse Lane, Birmingham B4 6NH, UK.
Radiol Case Rep. 2021 Mar 26;16(6):1237-1241. doi: 10.1016/j.radcr.2021.02.072. eCollection 2021 Jun.
In a male neonate with bilateral hydroureteronephrosis, the most common surgical diagnosis is posterior urethral valves. This case report describes a male infant with the same presentation, but caused by a very uncommon congenital anomaly. The summation of different imaging modalities allowed a multidisciplinary team of colleagues to define the anatomy: bilateral duplex kidneys draining into separate urinary bladders. Only one of the bladders had an outlet, hence the obstructive uropathy to the right kidney led to total loss of function. The distended tortuous ureters produced a mass effect at presentation. This case acts as a reminder that complex congenital anomalies can mimic the presentation of more common conditions, and that they often require input from various specialists to diagnose the condition and guide its management.
在一名患有双侧肾盂积水的男新生儿中，最常见的外科诊断是后尿道瓣膜。本病例报告描述了一名具有相同表现但由非常罕见的先天性异常引起的男婴。不同成像方式的综合运用使多学科团队的同事能够明确解剖结构：双侧重复肾分别引流至各自的膀胱。只有一个膀胱有出口，因此右肾的梗阻性尿路病导致其功能完全丧失。扩张迂曲的输尿管在就诊时产生了占位效应。本病例提醒我们，复杂的先天性异常可能会模仿更常见疾病的表现，而且它们通常需要各专科医生的参与来诊断病情并指导治疗。
