Aka F, Chantepie A, Vaillant M C, Pottier J M, Laugier J
Service de Pédiatrie A, Hôpital Clocheville, Tours.
Arch Fr Pediatr. 1988 Mar;45(3):181-5.
One hundred and thirty-three children less than one month of age and presenting with congenital heart disease were investigated using two-dimensional echocardiography (TD echo). In these children, 234 cardiovascular abnormalities had been proven by hemodynamic and angiographic investigations (n = 103), post-mortem examinations (n = 15) or operative findings (n = 12). TD echo identified 201 cardiovascular abnormalities with 33 false negatives (sensitivity 86%) and 12 false positives (specificity 94%). Diagnosis after TD echo was correct in 100 children (75%), incomplete in 18 (13.5%), imprecise in 11 (8.3%) and false in 4 (3%). The most frequently unrecognized lesions were: anomalous systemic venous drainage (5/8), persistent ductus arteriosus (5/12), pulmonary stenosis (3/8), ventricular septal defect (5/27), coarctation (2/18). The lesions difficult to characterize concerned mostly the pulmonary valve and the aspect of the aortic arch. On the other hand, TD echo allowed to correctly identify major intracardiac abnormalities, malpositions of the great vessels and to well appreciate the dimensions of the trunk and branches of the pulmonary artery. These results allow to refrain from diagnostic endocavitary investigations in most of the heart defects revealed in the neonatal period and to perform curative or palliative closed heart surgery without preoperative catheterization. However, clinical, angiographic and hemodynamic investigations keep an important place in the preoperative evaluation of defects that may benefit from open heart surgery.
对133例小于1个月龄且患有先天性心脏病的患儿进行了二维超声心动图(TD超声)检查。在这些患儿中,234处心血管异常已通过血流动力学和血管造影检查(n = 103)、尸检(n = 15)或手术结果(n = 12)得到证实。TD超声识别出201处心血管异常,有33例假阴性(敏感性86%)和12例假阳性(特异性94%)。TD超声检查后诊断正确的有100例患儿(75%),诊断不完整的有18例(13.5%),诊断不准确的有11例(8.3%),误诊的有4例(3%)。最常未被识别的病变为:体静脉引流异常(5/8)、动脉导管未闭(5/12)、肺动脉狭窄(3/8)、室间隔缺损(5/27)、主动脉缩窄(2/18)。难以定性的病变主要涉及肺动脉瓣和主动脉弓情况。另一方面,TD超声能够正确识别主要的心内异常、大血管错位,并能很好地评估肺动脉主干和分支的大小。这些结果使得在新生儿期发现的大多数心脏缺陷中无需进行诊断性心腔内检查,并且可以在不进行术前导管插入术的情况下进行根治性或姑息性心脏直视手术。然而,临床、血管造影和血流动力学检查在可能受益于心脏直视手术的缺陷术前评估中仍占有重要地位。