1型糖尿病Mauriac综合征中的持续性乳酸性酸中毒。
Persistent lactic acidosis in the Mauriac syndrome in type 1 diabetes mellitus.
作者信息
Subedi Abinash, Kumar Vishnu Charan Suresh, Sharma Anuj, Hoilat Gilles, John Savio
机构信息
Department of Internal Medicine, State University of New York Upstate Medical University, Syracuse, New York.
Division of Gastroenterology, State University of New York Upstate Medical University, Syracuse, New York.
出版信息
Proc (Bayl Univ Med Cent). 2021 Jan 11;34(3):382-383. doi: 10.1080/08998280.2020.1866936.
Abstract
Mauriac syndrome is an uncommon clinical condition arising in the setting of poorly controlled type 1 diabetes mellitus. Clinical features include hepatomegaly and liver abnormalities indistinguishable from nonalcoholic fatty liver disease. Early diagnosis and management are essential, as Mauriac syndrome is reversible.
摘要
莫里亚克综合征是一种在1型糖尿病控制不佳的情况下出现的罕见临床病症。临床特征包括肝肿大和与非酒精性脂肪性肝病难以区分的肝脏异常。由于莫里亚克综合征是可逆的，早期诊断和治疗至关重要。
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Four cases of type 1 diabetes mellitus showing sharp serum transaminase increases and hepatomegaly due to glycogenic hepatopathy.4例1型糖尿病患者因糖原性肝病出现血清转氨酶急剧升高和肝肿大。
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Diagnosis of hepatic glycogenosis in poorly controlled type 1 diabetes mellitus.控制不佳的1型糖尿病患者肝糖原累积症的诊断
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