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一例肾上腺危象诱发的应激性心肌病

A Case of Adrenal Crisis-Induced Stress Cardiomyopathy.

作者信息

Harris Chad L, Khalid Mazin, Hashmi Arsalan, Shani Jacob, Malik Bilal A

机构信息

Internal Medicine, Maimonides Medical Center, New York, USA.

Cardiology, Maimonides Medical Center, New York, USA.

出版信息

Cureus. 2021 Apr 11;13(4):e14420. doi: 10.7759/cureus.14420.

DOI:10.7759/cureus.14420
PMID:33996290
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC8117259/
Abstract

We report a case of a 36-year-old male who presented to the emergency department with complaints of weakness. On presentation the patient was hypotensive, hyperkalemic, and hyponatremic. The patient experienced a sudden cardiac arrest in the computed tomography (CT) scanner moments after arrival. Electrocardiogram (EKG) demonstrated PR prolongation and widened QRS. Echocardiogram demonstrated a left ventricular ejection fraction of 26%-30% with evidence of severe hypokinesis of the mid antero-septal and inferior-septal segments of the left ventricle. CT of the chest, abdomen, and pelvis demonstrated hypoplastic/atrophic adrenal glands. Total cortisol level was undetectable by lab measurement. The patient was diagnosed with stress cardiomyopathy secondary to adrenal crisis. He was managed with hydrocortisone and eventually made a full clinical recovery and improvement in left ventricular ejection fraction. This article references the rarity of this phenomenon and its relevance to early clinical detection.

摘要

我们报告一例36岁男性,因虚弱症状前往急诊科就诊。就诊时患者血压低、血钾高、血钠低。患者到达后不久在计算机断层扫描(CT)扫描仪中突发心脏骤停。心电图(EKG)显示PR间期延长和QRS波增宽。超声心动图显示左心室射血分数为26%-30%,左心室前间隔和下间隔中段有严重运动减弱的证据。胸部、腹部和骨盆的CT显示肾上腺发育不全/萎缩。实验室检测未检测到总皮质醇水平。该患者被诊断为继发于肾上腺危象的应激性心肌病。他接受了氢化可的松治疗,最终临床完全康复,左心室射血分数有所改善。本文提及了这种现象的罕见性及其与早期临床检测的相关性。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2b3c/8117259/d63f663a3587/cureus-0013-00000014420-i03.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2b3c/8117259/c0eb2f75eee1/cureus-0013-00000014420-i01.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2b3c/8117259/eacab44f427b/cureus-0013-00000014420-i02.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2b3c/8117259/d63f663a3587/cureus-0013-00000014420-i03.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2b3c/8117259/c0eb2f75eee1/cureus-0013-00000014420-i01.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2b3c/8117259/eacab44f427b/cureus-0013-00000014420-i02.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2b3c/8117259/d63f663a3587/cureus-0013-00000014420-i03.jpg

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本文引用的文献

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2
Clinical Features and Outcomes of Takotsubo (Stress) Cardiomyopathy.Takotsubo(应激性)心肌病的临床特征和转归。
N Engl J Med. 2015 Sep 3;373(10):929-38. doi: 10.1056/NEJMoa1406761.
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Systolic and diastolic mechanics in stress cardiomyopathy.应激性心肌病的收缩和舒张力学。
Circulation. 2014 Apr 22;129(16):1659-67. doi: 10.1161/CIRCULATIONAHA.113.002781. Epub 2014 Feb 6.
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