is an assistant professor, Department of Anesthesiology, Pain Medicine and Critical Care, All India Institute of Medical Sciences, New Delhi, India.
is an assistant professor, Department of Anesthesiology, Pain Medicine and Critical Care, All India Institute of Medical Sciences.
AANA J. 2021 Jun;89(3):195-199.
Klippel-Feil syndrome (KFS) is a rare congenital anomaly that is characterized by short neck, low posterior hairline, and restricted neck movements, all of which lead to the possibility of a difficult airway. These patients often have associated multiple systemic anomalies, which add to the challenges in anesthetic management. We describe the anesthetic management of 3 patients with KFS: 2 who underwent modified radical mastoidectomy and 1 patient who underwent vaginoplasty at our institute. Careful planning and preparedness for difficult airway and thorough knowledge of associated comorbidities are key to successful management of patients with KFS.
克莱佩尔-菲尔综合征(KFS)是一种罕见的先天性异常,其特征为短颈、低位后发际线和颈部活动受限,所有这些都导致气道困难的可能性增加。这些患者常伴有多种全身异常,这增加了麻醉管理的挑战。我们描述了在我院接受改良乳突根治术的 2 例患者和接受阴道成形术的 1 例患者的麻醉管理。对于 KFS 患者,成功管理的关键是仔细规划和准备困难气道以及深入了解相关合并症。