Ali Moeez, Riad Mohamed, Adhikari Prakash, Bhattarai Sanket, Gupta Ashish, Ali Eiman, Mostafa Jihan A
Internal Medicine, California Institute of Behavioral Neurosciences & Psychology, Fairfield, USA.
Internal Medicine, Piedmont Athens Regional Medical Center, Athens, USA.
Cureus. 2021 Apr 27;13(4):e14719. doi: 10.7759/cureus.14719.
Systemic lupus erythematosus (SLE) and myasthenia gravis (MG) are autoimmune states which have presentational similitude. Both conditions test serologically positive for anti-nuclear antibodies and require exceptional differential diagnostic acumen to segregate one from the other. The hypothesized factors provoking these diseases may be immunological, genetic, hormonal, or environmental and can be better understood by large-scale controlled epidemiological studies. Biochemical factors such as variation in CXC (an α chemokine subfamily), CXCL13, and granulocyte-macrophage colony-stimulating factor levels are assumed to play a pivotal role in the pathogenesis of SLE and MG; however, further studies are required to understand their exact mechanism and effect on the underlying autoimmune diseases. Following this, another precipitating factor for this overlap is believed to be thymectomy which is performed to eliminate MG symptoms. Although thymectomy is the effective treatment modality in MG patients, other findings and data support the view that this procedure may lead to the development of other autoimmune states such as SLE. It is evident from previously published data and case reports that patients with one autoimmune disease who underwent thymectomy contracted SLE and became more susceptible to other autoimmune diseases compared to the general population. Post-thymectomy follow-up of patients provides us with mechanistic clues for understanding the development of SLE-MG overlap; hence, in MG patients who have undergone thymectomy, any clinical and immune serological SLE suspicion should be carefully evaluated.
系统性红斑狼疮(SLE)和重症肌无力(MG)是具有相似临床表现的自身免疫状态。这两种疾病的抗核抗体血清学检测均呈阳性,需要具备非凡的鉴别诊断能力才能将两者区分开来。引发这些疾病的假定因素可能是免疫、遗传、激素或环境因素,大规模对照流行病学研究能更好地理解这些因素。诸如CXC(一种α趋化因子亚家族)、CXCL13和粒细胞巨噬细胞集落刺激因子水平变化等生化因素被认为在SLE和MG的发病机制中起关键作用;然而,需要进一步研究以了解它们的确切机制及其对潜在自身免疫性疾病的影响。在此之后,这种重叠的另一个促发因素被认为是为消除MG症状而进行的胸腺切除术。尽管胸腺切除术是MG患者的有效治疗方式,但其他研究结果和数据支持这样一种观点,即该手术可能导致其他自身免疫状态的发展,如SLE。从先前发表的数据和病例报告中可以明显看出,与普通人群相比,患有一种自身免疫性疾病且接受了胸腺切除术的患者会患上SLE,并更容易患上其他自身免疫性疾病。对患者进行胸腺切除术后的随访为我们提供了理解SLE - MG重叠发生发展的机制线索;因此,对于接受过胸腺切除术的MG患者,任何临床和免疫血清学方面对SLE的怀疑都应仔细评估。