Suzuki Yuji, Suzuki Akiko, Kakisaka Keisuke, Takikawa Yasuhiro
Division of Hepatology Department of Internal Medicine Iwate Medical University School of Medicine Yahaba-cho Japan.
Clin Case Rep. 2021 May 25;9(5):e04326. doi: 10.1002/ccr3.4326. eCollection 2021 May.
Acute Budd-Chiari syndrome and complete portal vein thrombosis are important features of myeloproliferative neoplasm that may occur simultaneously, resulting in acute liver failure. Liver transplantation could be effective even in such a catastrophic condition without post-transplant complications.
急性布加综合征和完全性门静脉血栓形成是骨髓增殖性肿瘤的重要特征,可能同时发生,导致急性肝衰竭。即使在这种灾难性情况下,肝移植也可能有效,且无移植后并发症。