Massie Emmanuelle, White Michel, Robillard Julie, Demers Philippe, Mondésert Blandine, Doyon Josée, Chaix Marie-A
Department of Medicine, Division of Cardiology, Montreal Heart institute, Université de Montréal, Montréal, Québec, Canada.
Department of Medicine, Division of Radiology, Montréal Heart Institute, Université de Montréal, Montréal, Québec, Canada.
CJC Open. 2021 Feb 4;3(6):831-834. doi: 10.1016/j.cjco.2021.01.010. eCollection 2021 Jun.
Primary pulmonary artery sarcoma is an exceedingly rare and aggressive malignancy that carries poor prognosis. Clinical manifestations are nonspecific and include chest pain, dyspnea, syncope, palpitations, and asthenia, among others. Delay to diagnosis is common and compromises the prognosis. Here, we report an interesting case of primary pulmonary artery sarcoma presenting with frequent monomorphic premature ventricular contractions arising from the right/left ventricle outflow tract. Cardiac imaging is key in the evaluation of patients with frequent premature ventricular contractions to rule out rare pathologies such as tumour compression.
原发性肺动脉肉瘤是一种极其罕见且侵袭性强的恶性肿瘤，预后较差。其临床表现无特异性，包括胸痛、呼吸困难、晕厥、心悸和乏力等。诊断延迟很常见，会影响预后。在此，我们报告一例有趣的原发性肺动脉肉瘤病例，该病例表现为右/左心室流出道频繁出现单形性室性早搏。心脏成像对于评估频繁室性早搏患者以排除肿瘤压迫等罕见病变至关重要。
