Kriz Joseph P, Munfakh Nabil A, King Gregory S, Carden Juan O
Christian Hospital, St. Louis, Mo., USA.
Case Rep Oncol. 2016 Apr 29;9(1):267-72. doi: 10.1159/000445498. eCollection 2016 Jan-Apr.
Pulmonary artery intimal sarcomas are rare and lethal malignant tumors that typically affect larger vessels: the aorta, inferior vena cava, and pulmonary arteries. Since symptoms and imaging of pulmonary arterial intimal sarcomas mimic pulmonary thromboembolism, the differential diagnosis of a patient presenting with chest pain, dyspnea, and filling defect within the pulmonary arteries should include intimal sarcoma. Often right ventricular failure is observed due to pulmonary hypertension caused by the obstructive effect of the tumor and concomitant chronic thromboembolism. We report the case of a 72-year-old African-American male with arterial intimal sarcoma of the left and right pulmonary artery with extension through the right artery into the bronchus and right lung.
肺动脉内膜肉瘤是一种罕见的致命性恶性肿瘤，通常累及较大血管：主动脉、下腔静脉和肺动脉。由于肺动脉内膜肉瘤的症状和影像学表现与肺血栓栓塞相似，因此对于出现胸痛、呼吸困难和肺动脉内充盈缺损的患者，鉴别诊断应包括内膜肉瘤。由于肿瘤的阻塞作用和并发的慢性血栓栓塞导致肺动脉高压，常可观察到右心衰竭。我们报告一例72岁非裔美国男性患者，其左右肺动脉均发生动脉内膜肉瘤，并通过右肺动脉延伸至支气管和右肺。
