Ukemenam Chinedu, Muppaneni Sivaram Prabhuji, De Debapriya, Lacasse Alexandre
Department of Internal Medicine, SSM Saint Mary's Hospital, Saint Louis, Missouri, USA.
J Community Hosp Intern Med Perspect. 2021 Jun 21;11(4):566-567. doi: 10.1080/20009666.2020.1816273.
Hugh-Stovin Syndrome (HSS) is characterized by recurrent thrombophlebitis and multiple pulmonary and/or bronchial artery aneurysms indistinguishable from the cardiovascular features seen in Behcet's disease (BD). Our case describes a 30-year-old male with recurrent pulmonary embolism and bilateral pulmonary aneurysms. Autoimmune, hypercoagulable, and infectious work up were negative. Elevated inflammatory markers and absence of the typical clinical findings seen in BD led to the diagnosis of Hugh-Stovin syndrome (HSS). Immunosuppression using steroids and azathioprine led to clinical response. Anticoagulation was continued based on risk/benefit ratio.
休-斯托文综合征（HSS）的特征为复发性血栓性静脉炎以及多发性肺和/或支气管动脉动脉瘤，其心血管特征与白塞病（BD）难以区分。我们的病例描述了一名30岁男性，患有复发性肺栓塞和双侧肺动脉瘤。自身免疫、高凝状态及感染相关检查均为阴性。炎症标志物升高且缺乏BD的典型临床表现，从而诊断为休-斯托文综合征（HSS）。使用类固醇和硫唑嘌呤进行免疫抑制治疗后出现临床反应。根据风险/获益比继续进行抗凝治疗。
