Watanabe Yukihiro, Akutsu Koichi, Yasui Daisuke, Sugihara Fumie, Miyachi Hideki, Hayashi Hiroshi, Oka Eiichiro, Komiyama Hidenori, Kumita Shin-Ichiro, Shimizu Wataru
Department of Cardiovascular Medicine, Nippon Medical School, Tokyo, Japan.
Department of Radiology, Nippon Medical School, Tokyo, Japan.
Ann Vasc Dis. 2021 Jun 25;14(2):163-167. doi: 10.3400/avd.cr.20-00144.
Vascular Ehlers-Danlos syndrome (vEDS) causes fatal vascular complications due to vascular fragility. However, invasive therapeutic procedures are generally avoided except in emergencies. We report a case of vEDS presenting with rapid expansion of a hepatic arterial aneurysm successfully treated using prophylactic endovascular therapy. A 43-year-old woman with vEDS confirmed by genetic testing was hospitalized for a symptomatic hepatic arterial aneurysm that expanded rapidly within a week. Prophylactic coil embolization was then successfully performed. Although the general applicability of this approach cannot be determined, prophylactic endovascular therapy can clearly be an option for arterial aneurysms at high risk of rupture.
血管型埃勒斯-当洛综合征（vEDS）因血管脆弱导致致命的血管并发症。然而，除紧急情况外，一般避免进行侵入性治疗操作。我们报告一例vEDS患者，其肝动脉动脉瘤迅速扩大，采用预防性血管内治疗成功治愈。一名经基因检测确诊为vEDS的43岁女性因有症状的肝动脉动脉瘤入院，该动脉瘤在一周内迅速扩大。随后成功进行了预防性弹簧圈栓塞术。虽然无法确定这种方法的普遍适用性，但预防性血管内治疗显然可以作为破裂风险高的动脉动脉瘤的一种选择。
