Tashiro K, Fukazawa T, Moriwaka F, Hamada T, Isu T, Iwasaki Y, Abe H
Division of Neurology, Hokkaido University School of Medicine, Sapporo, Japan.
J Neurol. 1987 Oct;235(1):26-30. doi: 10.1007/BF00314193.
The clinical features of 31 cases of syringomyelic syndrome, confirmed by metrizamide CT myelography (CTM) or magnetic resonance imaging (MRI), were analysed. Bilateral suspended sensory disturbance, previously regarded as a characteristic feature, was encountered in only 2 cases (6.5%). Thirteen patients (41.9%) showed no motor deficits of the upper limbs and 7 patients (22.6%) did not have weakness or atrophy in any of the four extremities. Cervical segmental signs were absent in 7 cases (22.6%) and in 2 (6.5%) signs were only present in the lower limbs. Scoliosis and foot deformity, such as pes cavus or equinovarus, were seen in 17 (54.8%) and 5 cases (16.1%) respectively. These skeletal abnormalities were initial symptoms in some childhood cases. In syringomyelic syndrome, clinical features are variable with many atypical clinical manifestations, apart from the previously recognized characteristic clinical features.
对经甲泛葡胺脊髓造影（CTM）或磁共振成像（MRI）确诊的31例脊髓空洞症综合征患者的临床特征进行了分析。双侧节段性感觉障碍，以前被视为特征性表现，仅在2例（6.5%）中出现。13例患者（41.9%）上肢无运动功能缺损，7例患者（22.6%）四肢均无无力或萎缩。7例（22.6%）无颈段体征，2例（6.5%）仅下肢有体征。分别有17例（54.8%）和5例（16.1%）出现脊柱侧弯和足部畸形，如高弓足或马蹄内翻足。这些骨骼异常在一些儿童病例中是首发症状。在脊髓空洞症综合征中，除了先前公认的特征性临床表现外，临床特征多变，有许多非典型临床表现。
